Table 4.

VWF concentrate administration

VWF concentrate optionDescription
VWF/FVIII concentrate (plasma derived) Plasma-derived concentrate containing both VWF and FVIII; administered IV; typical dosing: 40-80 VWF/RCo activity units per kg 
VWF concentrate (plasma derived) Plasma-derived concentrate containing VWF alone; administered IV; typical dosing: 40-80 VWF/RCo activity units per kg; if used for emergency treatment, may require addition of FVIII concentrate in patients with low baseline FVIII 
VWF concentrate (recombinant) Recombinant concentrate containing VWF alone; administered IV; typical dosing: 40-80 VWF/RCo activity units per kg; if used for emergency treatment, may require addition of FVIII concentrate in patients with low baseline FVIII 
VWF concentrate optionDescription
VWF/FVIII concentrate (plasma derived) Plasma-derived concentrate containing both VWF and FVIII; administered IV; typical dosing: 40-80 VWF/RCo activity units per kg 
VWF concentrate (plasma derived) Plasma-derived concentrate containing VWF alone; administered IV; typical dosing: 40-80 VWF/RCo activity units per kg; if used for emergency treatment, may require addition of FVIII concentrate in patients with low baseline FVIII 
VWF concentrate (recombinant) Recombinant concentrate containing VWF alone; administered IV; typical dosing: 40-80 VWF/RCo activity units per kg; if used for emergency treatment, may require addition of FVIII concentrate in patients with low baseline FVIII 

RCo, ristocetin cofactor.

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