Table 2.

Classification of LCH in adults

SubtypeDefinition
Unifocal Solitary lesion involving any organ 
Single-system pulmonary Isolated lung involvement (predominantly smoking related) 
Single-system multifocal >1 lesion involving any organ 
Multisystem ≥2 organ/system involvement 
SubtypeDefinition
Unifocal Solitary lesion involving any organ 
Single-system pulmonary Isolated lung involvement (predominantly smoking related) 
Single-system multifocal >1 lesion involving any organ 
Multisystem ≥2 organ/system involvement 

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