Table 2.
Classification of LCH in adults
Subtype
.
Definition
.
Unifocal
Solitary lesion involving any organ
Single-system pulmonary
Isolated lung involvement (predominantly smoking related)
Single-system multifocal
>1 lesion involving any organ
Multisystem
≥2 organ/system involvement
Subtype
.
Definition
.
Unifocal
Solitary lesion involving any organ
Single-system pulmonary
Isolated lung involvement (predominantly smoking related)
Single-system multifocal
>1 lesion involving any organ
Multisystem
≥2 organ/system involvement
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