Distribution of IEI-related comorbidities and age at HSCT by IEI subgroup
. | Group . | CID . | PAD . | PD . | P value . | |||
---|---|---|---|---|---|---|---|---|
Median (IQR) . | Median (IQR) . | Median (IQR) . | ||||||
Age at HSCT | Median (IQR) | 17.6 (16.4-21.2) | 22.8 (17.4-37.9) | 18.9 (16.8-22.5 | .001 | |||
Missing (%) | N (%) | Missing (%) | N (%) | Missing (%) | N (%) | P | ||
Hepatic comorbidity | No | 28 (17.2) | 113 (83.7) | 3 (7.7) | 27 (75.0) | 23 (18.1) | 99 (95.2) | .003 |
Mild | 11 (8.1) | 7 (19.4) | 4 (3.8) | |||||
Moderate/severe | 11 (8.1) | 2 (5.6) | 1 (1.0) | |||||
Splenectomy prior to HSCT | No | 5 (3.1) | 133 (84.2) | 4 (10.3) | 31 (88.6) | 5 (3.9) | 121 (99.2) | <.001 |
Yes | 25 (15.8) | 4 (11.4) | 1 (0.8) | |||||
Bronchiectasis at HSCT | Absent | 1 (0.6) | 119 (73.5) | 2 (5.1) | 21 (56.8) | 2 (1.6) | 98 (78.4) | .032 |
Present | 43 (26.5) | 16 (43.2) | 27 (21.6) | |||||
HCT-CI score | 0 | 5 (3.1) | 51 (32.3) | 1 (2.6) | 9 (23.7) | 1 (0.8) | 29 (23.0) | .096 |
1-2 | 56 (35.4) | 12 (31.6) | 60 (47.6) | |||||
>2 | 51 (32.3) | 17 (44.7) | 37 (29.4) |
. | Group . | CID . | PAD . | PD . | P value . | |||
---|---|---|---|---|---|---|---|---|
Median (IQR) . | Median (IQR) . | Median (IQR) . | ||||||
Age at HSCT | Median (IQR) | 17.6 (16.4-21.2) | 22.8 (17.4-37.9) | 18.9 (16.8-22.5 | .001 | |||
Missing (%) | N (%) | Missing (%) | N (%) | Missing (%) | N (%) | P | ||
Hepatic comorbidity | No | 28 (17.2) | 113 (83.7) | 3 (7.7) | 27 (75.0) | 23 (18.1) | 99 (95.2) | .003 |
Mild | 11 (8.1) | 7 (19.4) | 4 (3.8) | |||||
Moderate/severe | 11 (8.1) | 2 (5.6) | 1 (1.0) | |||||
Splenectomy prior to HSCT | No | 5 (3.1) | 133 (84.2) | 4 (10.3) | 31 (88.6) | 5 (3.9) | 121 (99.2) | <.001 |
Yes | 25 (15.8) | 4 (11.4) | 1 (0.8) | |||||
Bronchiectasis at HSCT | Absent | 1 (0.6) | 119 (73.5) | 2 (5.1) | 21 (56.8) | 2 (1.6) | 98 (78.4) | .032 |
Present | 43 (26.5) | 16 (43.2) | 27 (21.6) | |||||
HCT-CI score | 0 | 5 (3.1) | 51 (32.3) | 1 (2.6) | 9 (23.7) | 1 (0.8) | 29 (23.0) | .096 |
1-2 | 56 (35.4) | 12 (31.6) | 60 (47.6) | |||||
>2 | 51 (32.3) | 17 (44.7) | 37 (29.4) |