Table 5.

Percentages of progression to PSCR by genotype and sex

Progression to PSCR, N/total (%)P value 
HbSS/HbSβ0/HbSβ+ 5 of 79 (6.3) .841 
Male 2 of 35 (5.7)  
Female 3 of 44 (6.8)  
HbSC 9 of 33 (27.3) .022 
Male 7 of 15 (46.7)  
Female 2 of 18 (11.1)  
Progression to PSCR, N/total (%)P value 
HbSS/HbSβ0/HbSβ+ 5 of 79 (6.3) .841 
Male 2 of 35 (5.7)  
Female 3 of 44 (6.8)  
HbSC 9 of 33 (27.3) .022 
Male 7 of 15 (46.7)  
Female 2 of 18 (11.1)  

Pearson χ2.

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