Table 1.

Overview of important clinical studies in first line for PTCL and the representation of rare PTCL subtypes

Investigational agent usedTotal number of patientsEATL/MEITL, n (best response)SPTCL n (best response)HSTCL n (best response)Responses in other/unspecified subtypes in publication
Brentuximab + CHP followed by ASCT (EATL-001, Sibon et al)49  14 14 (ORR = 79%, CR = 64%, 2-y PFS = 63%, 2-y OS = 68%) 0 (0) 0 (0) NA 
Brentuximab + CHP followed by ASCT (ECHELON-2, Horwitz et al)106  452 3 (0) 0 (0) 0 (0)  
Romidepsin + CHOP vs CHOP (Bachy et al)107  421 16 (5 Ro-CHOP, 11 CHOP) (NR) 9 (7 Ro-CHOP, 2 CHOP) (NR) 2 (1 Ro-CHOP, 1 CHOP) No significant difference in PFS between Ro-CHOP and CHOP for “other” PTCL histologies 
CHOP/ICE/IVAC followed by Auto/Allo (Voss et al)99  14 0 (0) 0 (0) 14 (ORR =64%, CR = 35%, 5-y OS = 50%) NA 
CHOEP followed by Auto/Allo (Schmitz et al)54  103 3 (NR) 1 (NR) 2 (NR) 1 primary cutaneous γ/δ T-cell lymphoma (outcome NR) 
CHEOP followed by ASCT (NLG-T-01, d’Amore et al)46  160 21 (5-y PFS = 38%, 5-y OS = 48%) 6 (3-y OS = 44%)
∗3-y OS for SPTCL and HSTCL estimated as composite of all patients with SPTCL, HSTCL, and ENKTL 
5 (3-y OS = 44%)
∗3-y OS for SPTCL and HSTCL estimated as composite of all patients with SPTCL, HSTCL, and ENKTL 
5 patients with ENKTL 
Investigational agent usedTotal number of patientsEATL/MEITL, n (best response)SPTCL n (best response)HSTCL n (best response)Responses in other/unspecified subtypes in publication
Brentuximab + CHP followed by ASCT (EATL-001, Sibon et al)49  14 14 (ORR = 79%, CR = 64%, 2-y PFS = 63%, 2-y OS = 68%) 0 (0) 0 (0) NA 
Brentuximab + CHP followed by ASCT (ECHELON-2, Horwitz et al)106  452 3 (0) 0 (0) 0 (0)  
Romidepsin + CHOP vs CHOP (Bachy et al)107  421 16 (5 Ro-CHOP, 11 CHOP) (NR) 9 (7 Ro-CHOP, 2 CHOP) (NR) 2 (1 Ro-CHOP, 1 CHOP) No significant difference in PFS between Ro-CHOP and CHOP for “other” PTCL histologies 
CHOP/ICE/IVAC followed by Auto/Allo (Voss et al)99  14 0 (0) 0 (0) 14 (ORR =64%, CR = 35%, 5-y OS = 50%) NA 
CHOEP followed by Auto/Allo (Schmitz et al)54  103 3 (NR) 1 (NR) 2 (NR) 1 primary cutaneous γ/δ T-cell lymphoma (outcome NR) 
CHEOP followed by ASCT (NLG-T-01, d’Amore et al)46  160 21 (5-y PFS = 38%, 5-y OS = 48%) 6 (3-y OS = 44%)
∗3-y OS for SPTCL and HSTCL estimated as composite of all patients with SPTCL, HSTCL, and ENKTL 
5 (3-y OS = 44%)
∗3-y OS for SPTCL and HSTCL estimated as composite of all patients with SPTCL, HSTCL, and ENKTL 
5 patients with ENKTL 

ASCT, autologous stem cell transplant; CAR, chimeric antigen receptor; CHOP, cyclophosphamide, doxorubicin, vincristine, prednisone; ICE, ifosfamide, carboplatin, etoposide; NA, not applicable; NR, not reported; SD, stable disease.

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