Table 1.

Outcomes of genetic subgroups with VEN-based therapy

Molecular subgroupResponse (CR/CRi)MRD-negative CR/CRi (MFC)OS (median or 2-year)References
IDH1 66.7% (n  =  22/33) 42% (n  =  5/12) 10.2 mo Pollyea et al. CCR 2022;18 Pratz et al. AJH 202438  
IDH2 86% (n  =  43/50) 50% (n  =  16/32) 27.5 mo Pollyea et al. CCR 2022;18 Pratz et al. AJH 202438  
NPM1 66.7% (n  =  18/27) 88% (n  =  15/17) 2-year OS: 71.8%64  DiNardo et al. Blood 2020;11 Pratz et al. AJH 202438  
FLT3-ITD 63.3% (n  =  19/30) 53% (n   =   9/17) 9.9 mo Konopleva et al. CCR 202212  
FLT3-TKD 76.9% (n  =  10/13) 50% (n  =  2/4) 19.2 mo Konopleva et al. CCR 202212  
N/KRAS 45% (n  =  13/29) 12 mo Rivera et al. AJH 202251  
TP53 55% (n  =  21/38) 30% (n  =  6/20) 5.5-7.4 mo DiNardo et al. Blood 2020;11 Pollyea et al. CCR 202213  
Molecular subgroupResponse (CR/CRi)MRD-negative CR/CRi (MFC)OS (median or 2-year)References
IDH1 66.7% (n  =  22/33) 42% (n  =  5/12) 10.2 mo Pollyea et al. CCR 2022;18 Pratz et al. AJH 202438  
IDH2 86% (n  =  43/50) 50% (n  =  16/32) 27.5 mo Pollyea et al. CCR 2022;18 Pratz et al. AJH 202438  
NPM1 66.7% (n  =  18/27) 88% (n  =  15/17) 2-year OS: 71.8%64  DiNardo et al. Blood 2020;11 Pratz et al. AJH 202438  
FLT3-ITD 63.3% (n  =  19/30) 53% (n   =   9/17) 9.9 mo Konopleva et al. CCR 202212  
FLT3-TKD 76.9% (n  =  10/13) 50% (n  =  2/4) 19.2 mo Konopleva et al. CCR 202212  
N/KRAS 45% (n  =  13/29) 12 mo Rivera et al. AJH 202251  
TP53 55% (n  =  21/38) 30% (n  =  6/20) 5.5-7.4 mo DiNardo et al. Blood 2020;11 Pollyea et al. CCR 202213  

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