Principal diseases associated with LGL leukemia
| Autoimmune disorders . | Prevalence . | |
|---|---|---|
| Joint disorders | RA | 10%-18% |
| Rhizomelic pseudopolyarthritis | Sporadic | |
| Unclassified inflammatory arthritis | Sporadic | |
| Endocrinopathies | Hashimoto's disease | Sporadic |
| Cushing's syndrome | Sporadic | |
| Autoimmune polyglandular syndrome | Sporadic | |
| Connective tissue disorders | Sjögren's syndrome | 13% |
| Uveitis | Sporadic | |
| Systemic lupus erythematosus | Sporadic | |
| Muscular and neurological disorders | Polymyositis | Sporadic |
| Inclusion body myositis | Sporadic | |
| Peripheral neuropathy | Sporadic | |
| Lambert-Eaton syndrome | Sporadic | |
| Myasthenia gravis | Sporadic | |
| Skin disorders | Psoriasis | Sporadic |
| Livedoid vasculopathy | Sporadic | |
| Cutaneous vasculitis | Sporadic | |
| Cutaneous papules and nodules | Sporadic | |
| Vasculitis | Small-vessel vasculitis | Sporadic |
| Type 1/2 cryoglobulinemia vasculitis | Sporadic | |
| Glomerulonephritis | Sporadic | |
| Pulmonary artery hypertension | Sporadic | |
| Bowel disorders | Celiac disease | Sporadic |
| Inflammatory bowel disease | Sporadic | |
| Immunodeficiencies | Good syndrome | Sporadic |
| Adenosine deaminase deficiency | Sporadic | |
| Immune cytopenia | PRCA | 5%-7%a |
| Autoimmune hemolytic anemia | Sporadic | |
| Immune thrombocytopenia | 1%-2% | |
| Evans syndrome | Sporadic | |
| Autoimmune disorders . | Prevalence . | |
|---|---|---|
| Joint disorders | RA | 10%-18% |
| Rhizomelic pseudopolyarthritis | Sporadic | |
| Unclassified inflammatory arthritis | Sporadic | |
| Endocrinopathies | Hashimoto's disease | Sporadic |
| Cushing's syndrome | Sporadic | |
| Autoimmune polyglandular syndrome | Sporadic | |
| Connective tissue disorders | Sjögren's syndrome | 13% |
| Uveitis | Sporadic | |
| Systemic lupus erythematosus | Sporadic | |
| Muscular and neurological disorders | Polymyositis | Sporadic |
| Inclusion body myositis | Sporadic | |
| Peripheral neuropathy | Sporadic | |
| Lambert-Eaton syndrome | Sporadic | |
| Myasthenia gravis | Sporadic | |
| Skin disorders | Psoriasis | Sporadic |
| Livedoid vasculopathy | Sporadic | |
| Cutaneous vasculitis | Sporadic | |
| Cutaneous papules and nodules | Sporadic | |
| Vasculitis | Small-vessel vasculitis | Sporadic |
| Type 1/2 cryoglobulinemia vasculitis | Sporadic | |
| Glomerulonephritis | Sporadic | |
| Pulmonary artery hypertension | Sporadic | |
| Bowel disorders | Celiac disease | Sporadic |
| Inflammatory bowel disease | Sporadic | |
| Immunodeficiencies | Good syndrome | Sporadic |
| Adenosine deaminase deficiency | Sporadic | |
| Immune cytopenia | PRCA | 5%-7%a |
| Autoimmune hemolytic anemia | Sporadic | |
| Immune thrombocytopenia | 1%-2% | |
| Evans syndrome | Sporadic | |
In the West and 29%-48% in Asia.
AIHA, autoimmune hemolytic anemia; ITP, immune thrombocytopenia; T-CUS, T-cell clones of uncertain significance.