Categorization of mature T-cell lymphomas based on clinical phenotype
| Nodal |
| ALK-positive ALCL |
| ALK-negative ALCL |
| PTCL-NOS |
| Nodal TFH cell lymphoma, angioimmunoblastic type |
| Nodal TFH cell lymphoma, follicular type |
| Nodal TFH cell lymphoma, NOS |
| EBV+ nodal T- and NK-cell lymphoma |
| Extranodal |
| Hepatosplenic T-cell lymphoma |
| Extranodal NK/T-cell lymphoma |
| Enteropathy-associated T-cell lymphoma |
| Monomorphic epitheliotropic intestinal T-cell lymphoma |
| Intestinal T-cell lymphoma, NOS |
| Indolent T-cell lymphoma of the gastrointestinal tract |
| Indolent NK-cell LPD of the gastrointestinal tract |
| Breast implant-associated ALCL |
| Leukemic/systemic |
| Systemic EBV+ T-cell lymphoma of childhood |
| Systemic chronic active EBV disease |
| Aggressive NK-cell leukemia |
| Adult T-cell leukemia/lymphoma |
| T-large granular lymphocytic leukemia |
| NK-large granular lymphocytic leukemia |
| T-cell prolymphocytic leukemia |
| Sézary syndrome |
| Cutaneous |
| Mycosis fungoides |
| Primary cutaneous CD30+ T-cell LPD: lymphomatoid papulosis |
| Primary cutaneous CD30+ T-cell LPD: primary cutaneous ALCL |
| Subcutaneous panniculitis-like T-cell lymphoma |
| Primary cutaneous γ/δ T-cell lymphoma |
| Primary cutaneous CD4+ small or medium T-cell LPD |
| Hydroa vacciniforme LPD |
| Severe mosquito bite allergy |
| Primary cutaneous acral CD8+ LPD |
| Primary cutaneous CD8+ aggressive epidermotropic cytotoxic T-cell lymphoma |
| Primary cutaneous peripheral T-cell lymphoma, NOS |
| Nodal |
| ALK-positive ALCL |
| ALK-negative ALCL |
| PTCL-NOS |
| Nodal TFH cell lymphoma, angioimmunoblastic type |
| Nodal TFH cell lymphoma, follicular type |
| Nodal TFH cell lymphoma, NOS |
| EBV+ nodal T- and NK-cell lymphoma |
| Extranodal |
| Hepatosplenic T-cell lymphoma |
| Extranodal NK/T-cell lymphoma |
| Enteropathy-associated T-cell lymphoma |
| Monomorphic epitheliotropic intestinal T-cell lymphoma |
| Intestinal T-cell lymphoma, NOS |
| Indolent T-cell lymphoma of the gastrointestinal tract |
| Indolent NK-cell LPD of the gastrointestinal tract |
| Breast implant-associated ALCL |
| Leukemic/systemic |
| Systemic EBV+ T-cell lymphoma of childhood |
| Systemic chronic active EBV disease |
| Aggressive NK-cell leukemia |
| Adult T-cell leukemia/lymphoma |
| T-large granular lymphocytic leukemia |
| NK-large granular lymphocytic leukemia |
| T-cell prolymphocytic leukemia |
| Sézary syndrome |
| Cutaneous |
| Mycosis fungoides |
| Primary cutaneous CD30+ T-cell LPD: lymphomatoid papulosis |
| Primary cutaneous CD30+ T-cell LPD: primary cutaneous ALCL |
| Subcutaneous panniculitis-like T-cell lymphoma |
| Primary cutaneous γ/δ T-cell lymphoma |
| Primary cutaneous CD4+ small or medium T-cell LPD |
| Hydroa vacciniforme LPD |
| Severe mosquito bite allergy |
| Primary cutaneous acral CD8+ LPD |
| Primary cutaneous CD8+ aggressive epidermotropic cytotoxic T-cell lymphoma |
| Primary cutaneous peripheral T-cell lymphoma, NOS |
EBV, Epstein-Barr virus; LPD, lymphoproliferative disorder.