Clinical characteristics of patients with NTRK1-rearranged histiocytosis
Patients . | N = 50 . |
---|---|
Sex, n (%) | |
Male | 32 (64) |
Female | 18 (36) |
Age at diagnosis, median (range), y | 11.5 (0.0-73) |
0-10, n (%) | 23 (46) |
10-20, n (%) | 8 (16) |
20-50, n (%) | 10 (20) |
>50, n (%) | 9 (18) |
Disease extent, n (%) | |
Skin-limited lesions | 44 (88) |
Extracutaneous lesions | 6 (12) |
Patients with skin-limited disease, n (%) | |
No. of lesions | |
1 | 41 (93) |
2-5 | 2 (5) |
>5 | 1 (2) |
Location | |
Head and neck | 21 (48) |
Trunk | 12 (27) |
Upper limbs | 10 (23) |
Lower limbs | 6 (14) |
Mucosa | 0 (0) |
Patients . | N = 50 . |
---|---|
Sex, n (%) | |
Male | 32 (64) |
Female | 18 (36) |
Age at diagnosis, median (range), y | 11.5 (0.0-73) |
0-10, n (%) | 23 (46) |
10-20, n (%) | 8 (16) |
20-50, n (%) | 10 (20) |
>50, n (%) | 9 (18) |
Disease extent, n (%) | |
Skin-limited lesions | 44 (88) |
Extracutaneous lesions | 6 (12) |
Patients with skin-limited disease, n (%) | |
No. of lesions | |
1 | 41 (93) |
2-5 | 2 (5) |
>5 | 1 (2) |
Location | |
Head and neck | 21 (48) |
Trunk | 12 (27) |
Upper limbs | 10 (23) |
Lower limbs | 6 (14) |
Mucosa | 0 (0) |