Table 1.

Clinical characteristics of patients with NTRK1-rearranged histiocytosis

PatientsN = 50
Sex, n (%)  
Male 32 (64) 
Female 18 (36) 
Age at diagnosis, median (range), y 11.5 (0.0-73) 
0-10, n (%) 23 (46) 
10-20, n (%) 8 (16) 
20-50, n (%) 10 (20) 
>50, n (%) 9 (18) 
Disease extent, n (%)  
Skin-limited lesions 44 (88) 
Extracutaneous lesions 6 (12) 
Patients with skin-limited disease, n (%)  
No. of lesions  
41 (93) 
2-5 2 (5) 
>5 1 (2) 
Location  
Head and neck 21 (48) 
Trunk 12 (27) 
Upper limbs 10 (23) 
Lower limbs 6 (14) 
Mucosa 0 (0) 
PatientsN = 50
Sex, n (%)  
Male 32 (64) 
Female 18 (36) 
Age at diagnosis, median (range), y 11.5 (0.0-73) 
0-10, n (%) 23 (46) 
10-20, n (%) 8 (16) 
20-50, n (%) 10 (20) 
>50, n (%) 9 (18) 
Disease extent, n (%)  
Skin-limited lesions 44 (88) 
Extracutaneous lesions 6 (12) 
Patients with skin-limited disease, n (%)  
No. of lesions  
41 (93) 
2-5 2 (5) 
>5 1 (2) 
Location  
Head and neck 21 (48) 
Trunk 12 (27) 
Upper limbs 10 (23) 
Lower limbs 6 (14) 
Mucosa 0 (0) 

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