Table 1.

Patient characteristics

No. of patients N = 100 
Age at diagnosis  
Years, median (range) 10.9 (1.4-17.3) 
Gender, n (%)  
Male 54 (54) 
Female 46 (46) 
Blood count at diagnosis  
Hb  
g/dL, median (range), n = 92 10.5 (3.9-16) 
n (%)  
≥12 g/dL 24 (24) 
10 to <12 g/dL 35 (35) 
7 to <10 g/dL 20 (20) 
<7 g/dL 13 (13) 
RBC transfused, no data on Hb before transfusion 7 (7) 
Not evaluable (no data about transfusion) 1 (1) 
White blood cell count  
× 109/L, median (range), n = 99 3.5 (0.3-7.7) 
ANCs  
× 109/L, median (range), n = 92 1.1 (0-4.8) 
n (%)  
≥1.5 × 109/L 28 (28) 
1.0 to <1.5 × 109/L 21 (21) 
0.5 to <1.0 × 109/L 34 (34) 
<0.5 × 109/L 9 (0) 
No data 8 (8) 
PLT count  
× 109/L, median (range), n = 85 56 (1-427) 
n (%)  
≥150 × 109/L 11 (11) 
100 to <150 × 109/L 12 (12) 
50 to <100 × 109/L 23 (23) 
20 to <50 × 109/L 29 (29) 
<20 × 109/L 10 (10) 
PLT transfused (no data on PLT count before transfusion) 14 (14) 
No data of PLT count 1 (1) 
MCV, n (%)  
Normal for age 45 (45) 
Elevated for age 43 (43) 
RBC transfused 7 (7) 
No data of MCV 5 (5) 
BM cellularity at diagnosis, n (%)  
Hypocellular 84 (84) 
Normocellular 12 (12) 
Hypercellular 4 (4) 
Karyotype, n (%)  
Normal by metaphase analysis 95 (95) 
No metaphase; FISH: absence of −7, del(7), +8 4 (4) 
No result 1 (1) 
Median follow-up  
Years (range) 7.2 (2.0-18.4) 
No. of patients N = 100 
Age at diagnosis  
Years, median (range) 10.9 (1.4-17.3) 
Gender, n (%)  
Male 54 (54) 
Female 46 (46) 
Blood count at diagnosis  
Hb  
g/dL, median (range), n = 92 10.5 (3.9-16) 
n (%)  
≥12 g/dL 24 (24) 
10 to <12 g/dL 35 (35) 
7 to <10 g/dL 20 (20) 
<7 g/dL 13 (13) 
RBC transfused, no data on Hb before transfusion 7 (7) 
Not evaluable (no data about transfusion) 1 (1) 
White blood cell count  
× 109/L, median (range), n = 99 3.5 (0.3-7.7) 
ANCs  
× 109/L, median (range), n = 92 1.1 (0-4.8) 
n (%)  
≥1.5 × 109/L 28 (28) 
1.0 to <1.5 × 109/L 21 (21) 
0.5 to <1.0 × 109/L 34 (34) 
<0.5 × 109/L 9 (0) 
No data 8 (8) 
PLT count  
× 109/L, median (range), n = 85 56 (1-427) 
n (%)  
≥150 × 109/L 11 (11) 
100 to <150 × 109/L 12 (12) 
50 to <100 × 109/L 23 (23) 
20 to <50 × 109/L 29 (29) 
<20 × 109/L 10 (10) 
PLT transfused (no data on PLT count before transfusion) 14 (14) 
No data of PLT count 1 (1) 
MCV, n (%)  
Normal for age 45 (45) 
Elevated for age 43 (43) 
RBC transfused 7 (7) 
No data of MCV 5 (5) 
BM cellularity at diagnosis, n (%)  
Hypocellular 84 (84) 
Normocellular 12 (12) 
Hypercellular 4 (4) 
Karyotype, n (%)  
Normal by metaphase analysis 95 (95) 
No metaphase; FISH: absence of −7, del(7), +8 4 (4) 
No result 1 (1) 
Median follow-up  
Years (range) 7.2 (2.0-18.4) 

BM, bone marrow; FISH, florescence in situ hybridization; PLT, platelet; RBC, red blood cell.

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