Patient demographics and baseline characteristics
| Characteristic . | N = 15 . |
|---|---|
| Mean age (range), y | 39 (25-57) |
| Sex, n (%) | |
| Female | 5 (33.3) |
| Male | 10 (66.7) |
| African or African American race, n (%) | 15 (100) |
| HbSS genotype, n (%) | 15 (100) |
| HU use, n (%) | 11 (73.3) |
| l-Glutamine use, n (%) | 0 (0.0) |
| Baseline laboratory measures | |
| Mean Hb (SD), g/dL | 8.80 (0.99) |
| Mean absolute reticulocyte count (SD), ×103/μL | 217.21 (88.27) |
| Mean total bilirubin (SD), mg/dL | 2.73 (1.43) |
| Mean lactate dehydrogenase (SD), U/L | 536.71 (222.16) |
| Median HbF (25th, 75th percentile), % | 13.80 (7.40, 23.95) |
| Characteristic . | N = 15 . |
|---|---|
| Mean age (range), y | 39 (25-57) |
| Sex, n (%) | |
| Female | 5 (33.3) |
| Male | 10 (66.7) |
| African or African American race, n (%) | 15 (100) |
| HbSS genotype, n (%) | 15 (100) |
| HU use, n (%) | 11 (73.3) |
| l-Glutamine use, n (%) | 0 (0.0) |
| Baseline laboratory measures | |
| Mean Hb (SD), g/dL | 8.80 (0.99) |
| Mean absolute reticulocyte count (SD), ×103/μL | 217.21 (88.27) |
| Mean total bilirubin (SD), mg/dL | 2.73 (1.43) |
| Mean lactate dehydrogenase (SD), U/L | 536.71 (222.16) |
| Median HbF (25th, 75th percentile), % | 13.80 (7.40, 23.95) |
HbF, fetal Hb; SD, standard deviation.