Table 1.

Demographic and baseline characteristics

HHT cohort characteristicsn (%)
Age (n = 22), y, mean (SD) 55.5 (17.2) 
Sex (n = 22)  
Male 12 (54.5) 
Female 10 (45.5) 
Race (n = 22)  
White 19 (86.4) 
African American 1 (4.5) 
Other 2 (9.1) 
Genotype (n = 22)  
ACVRL1 9 (40.9) 
ENG 7 (31.8) 
Unknown 6 (27.3) 
ESS (n = 26), mean (SD) 5.0 (1.6) 
Hemoglobin (n = 13), g/dL, mean (SD) 11.3 (SD 2.8) 
Hematocrit (n = 10), %, mean (SD) 37.5 (SD 7.0) 
HHT cohort characteristicsn (%)
Age (n = 22), y, mean (SD) 55.5 (17.2) 
Sex (n = 22)  
Male 12 (54.5) 
Female 10 (45.5) 
Race (n = 22)  
White 19 (86.4) 
African American 1 (4.5) 
Other 2 (9.1) 
Genotype (n = 22)  
ACVRL1 9 (40.9) 
ENG 7 (31.8) 
Unknown 6 (27.3) 
ESS (n = 26), mean (SD) 5.0 (1.6) 
Hemoglobin (n = 13), g/dL, mean (SD) 11.3 (SD 2.8) 
Hematocrit (n = 10), %, mean (SD) 37.5 (SD 7.0) 

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