Table 2.

MVA for OS

IWG classIWG class incl. BM blastsICCWHO5
ClassHRP valueClassHRP valueEntityHRP valueEntityHRP value
AML-like 0.319 .12 AML-like 0.277 .09 AML 0.627 .52 AML 0.542 .30 
BCOR/L1 0.891 .78 BCOR/L1 0.835 .68 CMML1 0.768 .26 CMML1 0.871 .55 
DDX41 0.663 .39 DDX41 0.577 .26 CMML2 2.644 .018 CMML2 3.460 .0009 
EZH2-ASXL1 1.123 .79 EZH2-ASXL1 1.150 .74 MDS-EB 0.954 .82 MDS-IB1 1.090 .68 
IDH-STAG2 0.717 .27 IDH-STAG2 0.679 .20 MDS/AML 1.112 .65 MDS-IB2 1.141 .59 
No-event 0.609 .18 No-event 0.575 .14 MDS-SF3B1 0.237 < .0001 MDS-SF3B1 0.283 < .0001 
−7/SETBP1 2.465 .015 −7/SETBP1 2.407 .0180 MDS-SLD 0.607 .11 MDS-hypoplastic 1.842 .16 
SF3B1 0.266 .0003 SF3B1 0.271 .0004 MDS-TP53 3.353 < .0001 MDS–bi-TP53 4.307 < .0001 
SRSF2 0.406 .38 SRSF2 0.406 .38 MDS-del5q 0.393 .02 MDS-del5q 0.484 .07 
TP53-CK 2.766 .0002 TP53-CK 2.555 .0008 SCT 0.291 < .0001 MDS-fibrosis 1.366 .55 
U2AF1-157 1.319 .54 U2AF1-157 1.283 .58    SCT 0.289 < .0001 
U2AF1-34 0.567 .24 U2AF1-34 0.548 .20       
ZRSR2 3.347 .06 ZRSR2 3.452 .05       
bi-TET2 0.479 .0495 bi-TET2 0.485 .05       
Del(5q) 0.363 .015 Del(5q) 0.360 .0147       
Der(1;7) 0.532 .54 Der(1;7) 0.530 .53       
mNOS 0.591 .17 mNOS 0.600 .18       
SCT 0.295 < .0001 SCT 0.277 < .0001       
   BM Blasts 1.020 .14       
IWG classIWG class incl. BM blastsICCWHO5
ClassHRP valueClassHRP valueEntityHRP valueEntityHRP value
AML-like 0.319 .12 AML-like 0.277 .09 AML 0.627 .52 AML 0.542 .30 
BCOR/L1 0.891 .78 BCOR/L1 0.835 .68 CMML1 0.768 .26 CMML1 0.871 .55 
DDX41 0.663 .39 DDX41 0.577 .26 CMML2 2.644 .018 CMML2 3.460 .0009 
EZH2-ASXL1 1.123 .79 EZH2-ASXL1 1.150 .74 MDS-EB 0.954 .82 MDS-IB1 1.090 .68 
IDH-STAG2 0.717 .27 IDH-STAG2 0.679 .20 MDS/AML 1.112 .65 MDS-IB2 1.141 .59 
No-event 0.609 .18 No-event 0.575 .14 MDS-SF3B1 0.237 < .0001 MDS-SF3B1 0.283 < .0001 
−7/SETBP1 2.465 .015 −7/SETBP1 2.407 .0180 MDS-SLD 0.607 .11 MDS-hypoplastic 1.842 .16 
SF3B1 0.266 .0003 SF3B1 0.271 .0004 MDS-TP53 3.353 < .0001 MDS–bi-TP53 4.307 < .0001 
SRSF2 0.406 .38 SRSF2 0.406 .38 MDS-del5q 0.393 .02 MDS-del5q 0.484 .07 
TP53-CK 2.766 .0002 TP53-CK 2.555 .0008 SCT 0.291 < .0001 MDS-fibrosis 1.366 .55 
U2AF1-157 1.319 .54 U2AF1-157 1.283 .58    SCT 0.289 < .0001 
U2AF1-34 0.567 .24 U2AF1-34 0.548 .20       
ZRSR2 3.347 .06 ZRSR2 3.452 .05       
bi-TET2 0.479 .0495 bi-TET2 0.485 .05       
Del(5q) 0.363 .015 Del(5q) 0.360 .0147       
Der(1;7) 0.532 .54 Der(1;7) 0.530 .53       
mNOS 0.591 .17 mNOS 0.600 .18       
SCT 0.295 < .0001 SCT 0.277 < .0001       
   BM Blasts 1.020 .14       

The analyses included SCT as a time-dependent variable for IWG class (left columns), ICC MDS entities (middle columns), and WHO5 MDS entities (right columns). BM blasts at diagnosis as a continuous variable were also included for the IWG analysis. Statistically significant entities within each classification are bolded. Reference groups: IWG: CCUS-like, ICC: MDS-MLD, WHO5: MDS-LB.

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