Baseline characteristics
| Variable . | Completed V1 (n = 42)∗ . | Completed V2 (n = 28)∗ . | Did not complete V2 (n = 14) . |
|---|---|---|---|
| Age, median (IQR), y | 47.5 (34.25-54.25) | 48 (35-53) | 44 (29-57) |
| Female sex | 78.6% | 75% | 85.7% |
| Black race | 71.4% | 78.6% | 57.1% |
| Time from iTTP diagnosis, median (IQR), mo | 41 (7.5-89.5) | 50 (6-109) | 39 (13-76) |
| Hypertension | 35.7% | 39.3% | 28.6% |
| Diabetes mellitus | 16.7% | 21.4% | 7.1% |
| Stroke during iTTP | 23.8% | 28.6% | 14.3% |
| Any SCI at V1 | 69% (29/42) | 68% (19/28) | 71.4% (10/14) |
| ARWMC score (for SCI) at V1, median (IQR) | 4 (0-7) | 3 (0-7) | 4 (0-7) |
| Time between MRI1 and MRI2, median (range), mo | — | 12.5 (12-14) | — |
| Average ADAMTS13 activity between V1 and V2, median (IQR) | — | 73.4 (58.2-95.7) | — |
| Variable . | Completed V1 (n = 42)∗ . | Completed V2 (n = 28)∗ . | Did not complete V2 (n = 14) . |
|---|---|---|---|
| Age, median (IQR), y | 47.5 (34.25-54.25) | 48 (35-53) | 44 (29-57) |
| Female sex | 78.6% | 75% | 85.7% |
| Black race | 71.4% | 78.6% | 57.1% |
| Time from iTTP diagnosis, median (IQR), mo | 41 (7.5-89.5) | 50 (6-109) | 39 (13-76) |
| Hypertension | 35.7% | 39.3% | 28.6% |
| Diabetes mellitus | 16.7% | 21.4% | 7.1% |
| Stroke during iTTP | 23.8% | 28.6% | 14.3% |
| Any SCI at V1 | 69% (29/42) | 68% (19/28) | 71.4% (10/14) |
| ARWMC score (for SCI) at V1, median (IQR) | 4 (0-7) | 3 (0-7) | 4 (0-7) |
| Time between MRI1 and MRI2, median (range), mo | — | 12.5 (12-14) | — |
| Average ADAMTS13 activity between V1 and V2, median (IQR) | — | 73.4 (58.2-95.7) | — |
MRI1, MRI at V1; MRI2, MRI at V2; V1, visit 1; V2, visit 2.
The group that completed V2 is a subset of the group that completed V1.