Table 2.

Conditions associated with both intravascular hemolysis and increased risk for pulmonary hypertension.

Hereditary hemolytic anemia 
    Sickle cell disease 
    Thalassemia 
    Hereditary spherocytosis 
    Hereditary stomatocytosis 
    Pyruvate kinase deficiency 
    Unstable hemoglobin variants 
Acquired hemolytic anemia 
    Microangiopathic hemolytic anemias 
    Paroxysmal nocturnal hemoglobinuria 
    Schistosomiasis 
    Mechanical heart valves 
    Left ventricular assist devices 
    Cardiopulmonary bypass devices 
    Malaria (?) 
Hereditary hemolytic anemia 
    Sickle cell disease 
    Thalassemia 
    Hereditary spherocytosis 
    Hereditary stomatocytosis 
    Pyruvate kinase deficiency 
    Unstable hemoglobin variants 
Acquired hemolytic anemia 
    Microangiopathic hemolytic anemias 
    Paroxysmal nocturnal hemoglobinuria 
    Schistosomiasis 
    Mechanical heart valves 
    Left ventricular assist devices 
    Cardiopulmonary bypass devices 
    Malaria (?) 
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