WHO 2008 classification of mature T/NK-cell neoplasms.2
* designates provisional entities |
Leukemic or disseminated |
T-cell prolymphocytic leukemia |
T-cell large granular lymphocytic leukemia |
Chronic lymphoproliferative disorders of NK cells* |
Aggressive NK-cell leukemia |
Adult T-cell lymphoma/leukemia (HTLV1-positive) |
Systemic Epstein-Barr virus (EBV)–positive T-cell lymphoproliferative disorders of childhood |
Extranodal |
Extranodal NK/T-cell lymphoma, nasal type |
Enteropathy-associated T-cell lymphoma |
Hepatosplenic T-cell lymphoma |
Extranodal—cutaneous |
Mycosis fungoides |
Sézary syndrome |
Primary cutaneous CD30+ lymphoproliferative disorders |
Primary cutaneous anaplastic large cell lymphoma |
Lymphomatoid papulosis |
Subcutaneous panniculitis-like T-cell lymphoma |
Primary cutaneous γδ T-cell lymphoma* |
Primary cutaneous aggressive epidermotropic CD8+ cytotoxic T-cell lymphoma* |
Primary cutaneous small/medium CD4+ T-cell lymphoma* |
Nodal |
Angioimmunoblastic T-cell lymphoma |
Anaplastic large cell lymphoma, ALK-positive |
Anaplastic large cell lymphoma, ALK-negative* |
Peripheral T-cell lymphoma, not otherwise specified |
* designates provisional entities |
Leukemic or disseminated |
T-cell prolymphocytic leukemia |
T-cell large granular lymphocytic leukemia |
Chronic lymphoproliferative disorders of NK cells* |
Aggressive NK-cell leukemia |
Adult T-cell lymphoma/leukemia (HTLV1-positive) |
Systemic Epstein-Barr virus (EBV)–positive T-cell lymphoproliferative disorders of childhood |
Extranodal |
Extranodal NK/T-cell lymphoma, nasal type |
Enteropathy-associated T-cell lymphoma |
Hepatosplenic T-cell lymphoma |
Extranodal—cutaneous |
Mycosis fungoides |
Sézary syndrome |
Primary cutaneous CD30+ lymphoproliferative disorders |
Primary cutaneous anaplastic large cell lymphoma |
Lymphomatoid papulosis |
Subcutaneous panniculitis-like T-cell lymphoma |
Primary cutaneous γδ T-cell lymphoma* |
Primary cutaneous aggressive epidermotropic CD8+ cytotoxic T-cell lymphoma* |
Primary cutaneous small/medium CD4+ T-cell lymphoma* |
Nodal |
Angioimmunoblastic T-cell lymphoma |
Anaplastic large cell lymphoma, ALK-positive |
Anaplastic large cell lymphoma, ALK-negative* |
Peripheral T-cell lymphoma, not otherwise specified |