WHO-EORTC classification for primary cutaneous lymphomas and associated frequency and 5-year survival.1
| WHO-EORTC . | Frequency (%) . | 5-year Survival (%) . |
|---|---|---|
| Cutaneous T-cell and NK-cell lymphoma | ||
| Indolent | ||
| Mycosis fungoides | 44 | 88 |
| Follicular MF | 4 | 80 |
| Pagetoid reticulosis | < 1 | 100 |
| Granulomatous slack skin | < 1 | 100 |
| CD30+ lymphoproliferative diseases | ||
| Anaplastic large cell lymphoma | 8 | 95 |
| Lymphomatoid papulosis | 12 | 100 |
| Subcutaneous panniculitis-like T-cell lymphoma | 1 | 82 |
| CD4+ small/medium pleomorphic T-cell lymphoma | 2 | 72 |
| Agressive | ||
| Sézary syndrome | 3 | 24 |
| Cutaneous aggressive CD8+ T-cell lymphoma | < 1 | 18 |
| Cutaneous γ/δ T-cell lymphoma | < 1 | — |
| Cutaneous peripheral T-cell lymphoma unspecified | 2 | 16 |
| Cutaneous NK/T-cell lymphoma, nasal-type | < 1 | — |
| WHO-EORTC . | Frequency (%) . | 5-year Survival (%) . |
|---|---|---|
| Cutaneous T-cell and NK-cell lymphoma | ||
| Indolent | ||
| Mycosis fungoides | 44 | 88 |
| Follicular MF | 4 | 80 |
| Pagetoid reticulosis | < 1 | 100 |
| Granulomatous slack skin | < 1 | 100 |
| CD30+ lymphoproliferative diseases | ||
| Anaplastic large cell lymphoma | 8 | 95 |
| Lymphomatoid papulosis | 12 | 100 |
| Subcutaneous panniculitis-like T-cell lymphoma | 1 | 82 |
| CD4+ small/medium pleomorphic T-cell lymphoma | 2 | 72 |
| Agressive | ||
| Sézary syndrome | 3 | 24 |
| Cutaneous aggressive CD8+ T-cell lymphoma | < 1 | 18 |
| Cutaneous γ/δ T-cell lymphoma | < 1 | — |
| Cutaneous peripheral T-cell lymphoma unspecified | 2 | 16 |
| Cutaneous NK/T-cell lymphoma, nasal-type | < 1 | — |