Table 1.

Repertoire of kinase rearrangements in Ph-like ALL along with their partner genes and potential therapeutic targets

Kinases5′ partner genes (number of patients)Potential TKIClinical trials
ABL1 ETV6 (3), NUP214 (6), RCSD1 (1), RANBP2 (1), SNX2 (1), ZMIZ1 (2) Dasatinib AALL1131 
ABL2 PAG1 (1), RCSD1 (4), ZC3HAV1 (2) Dasatinib AALL1131 
PDGFRB EBF1 (6), SSBP2 (1), TNIP1 (1), ZEB2 (1) Dasatinib AALL1131 
CSF1R SSBP2 (4) Dasatinib AALL1131 
CRLF2 IGH (19), P2RY8 (11) Ruxolitinib AALL1521 
JAK2 ATF7IP (1), BCR (2), EBF1 (1), ETV6 (2), PAX5 (7), PPFIBP1 (1), SSBP2 (2), STRN3 (1), TERF2 (1), TPR (1) Ruxolitinib AALL1521 
EPOR IGH (7), IGK (2) Ruxolitinib AALL1521 
TSLP IQGAP2 (1) Ruxolitinib AALL1521 
IL2RB MYH9 (1) JAK1/JAK3 inhibitor N/A 
TYK2 MYB (1) TYK2 inhibitor N/A 
NTRK3 ETV6 (1) Crizotinib N/A 
PTK2B KDM6A (1), STAG2 (1) FAK inhibitor N/A 
DGKH ZFAND3 (1) Unknown N/A 
Kinases5′ partner genes (number of patients)Potential TKIClinical trials
ABL1 ETV6 (3), NUP214 (6), RCSD1 (1), RANBP2 (1), SNX2 (1), ZMIZ1 (2) Dasatinib AALL1131 
ABL2 PAG1 (1), RCSD1 (4), ZC3HAV1 (2) Dasatinib AALL1131 
PDGFRB EBF1 (6), SSBP2 (1), TNIP1 (1), ZEB2 (1) Dasatinib AALL1131 
CSF1R SSBP2 (4) Dasatinib AALL1131 
CRLF2 IGH (19), P2RY8 (11) Ruxolitinib AALL1521 
JAK2 ATF7IP (1), BCR (2), EBF1 (1), ETV6 (2), PAX5 (7), PPFIBP1 (1), SSBP2 (2), STRN3 (1), TERF2 (1), TPR (1) Ruxolitinib AALL1521 
EPOR IGH (7), IGK (2) Ruxolitinib AALL1521 
TSLP IQGAP2 (1) Ruxolitinib AALL1521 
IL2RB MYH9 (1) JAK1/JAK3 inhibitor N/A 
TYK2 MYB (1) TYK2 inhibitor N/A 
NTRK3 ETV6 (1) Crizotinib N/A 
PTK2B KDM6A (1), STAG2 (1) FAK inhibitor N/A 
DGKH ZFAND3 (1) Unknown N/A 

Adapted from Roberts et al, with permission.

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