Characteristics of patients enrolled in the International Fanconi Anemia Registry (1982–2001)
| Variable . | No. patients (%) . |
|---|---|
| Sex | |
| Female | 367 (49) |
| Male | 387 (51) |
| Complementation group | |
| A | 207 (27) |
| C | 78 (10) |
| D2 | 2 (0.3) |
| F | 8 (1) |
| G | 46 (6) |
| Nontyped* | 413 (55) |
| BMF | |
| Yes | 601 (80) |
| No | 153 (20) |
| HSCT | |
| Yes | 219 (29) |
| No | 535 (71) |
| Hematologic malignancy | |
| Yes | 120 (16) |
| No | 634 (84) |
| Solid tumor | |
| Yes | 73 (10) |
| No | 681 (90) |
| Alive | |
| Yes | 471 (62) |
| No | 283 (38) |
| Variable . | No. patients (%) . |
|---|---|
| Sex | |
| Female | 367 (49) |
| Male | 387 (51) |
| Complementation group | |
| A | 207 (27) |
| C | 78 (10) |
| D2 | 2 (0.3) |
| F | 8 (1) |
| G | 46 (6) |
| Nontyped* | 413 (55) |
| BMF | |
| Yes | 601 (80) |
| No | 153 (20) |
| HSCT | |
| Yes | 219 (29) |
| No | 535 (71) |
| Hematologic malignancy | |
| Yes | 120 (16) |
| No | 634 (84) |
| Solid tumor | |
| Yes | 73 (10) |
| No | 681 (90) |
| Alive | |
| Yes | 471 (62) |
| No | 283 (38) |
HSCT indicates hematopoietic stem cell transplantation.
Complementation group unknown.