Clinical features at diagnosis according to the primary localization
| Extranodal site . | Overall . | Elevated LDH level . | Nodal disease . | Stage IV . | B symptoms . | Poor-risk IPI . | Bone marrow . |
|---|---|---|---|---|---|---|---|
| Skin | 22 | 2 | 0 | 4 | 0 | 2 | 2 |
| Orbit | 13 | 6 | 3 | 4 | 1 | 4 | 4 |
| Conjunctiva | 18 | 2 | 0 | 0 | 0 | 0 | 0 |
| Salivary glands | 46 | 8 | 5 | 4 | 1 | 3 | 4 |
| Lung | 15 | 4 | 4 | 3 | 0 | 2 | 1 |
| Upper airways | 12 | 5 | 4 | 4 | 0 | 3 | 4 |
| Breast | 3 | 1 | 0 | 0 | 0 | 0 | 0 |
| Thyroid | 10 | 1 | 4 | 0 | 0 | 0 | 0 |
| Urinary tract | 2 | 0 | 0 | 0 | 0 | 0 | 0 |
| Liver | 6 | 1 | 3 | 6 | 1 | 1 | 2 |
| Bowel | 9 | 1 | 4 | 0 | 1 | 0 | 0 |
| Multiple MALT sites | 24 | 6 | 11 | 24 | 1 | 16 | 8 |
| Extranodal site . | Overall . | Elevated LDH level . | Nodal disease . | Stage IV . | B symptoms . | Poor-risk IPI . | Bone marrow . |
|---|---|---|---|---|---|---|---|
| Skin | 22 | 2 | 0 | 4 | 0 | 2 | 2 |
| Orbit | 13 | 6 | 3 | 4 | 1 | 4 | 4 |
| Conjunctiva | 18 | 2 | 0 | 0 | 0 | 0 | 0 |
| Salivary glands | 46 | 8 | 5 | 4 | 1 | 3 | 4 |
| Lung | 15 | 4 | 4 | 3 | 0 | 2 | 1 |
| Upper airways | 12 | 5 | 4 | 4 | 0 | 3 | 4 |
| Breast | 3 | 1 | 0 | 0 | 0 | 0 | 0 |
| Thyroid | 10 | 1 | 4 | 0 | 0 | 0 | 0 |
| Urinary tract | 2 | 0 | 0 | 0 | 0 | 0 | 0 |
| Liver | 6 | 1 | 3 | 6 | 1 | 1 | 2 |
| Bowel | 9 | 1 | 4 | 0 | 1 | 0 | 0 |
| Multiple MALT sites | 24 | 6 | 11 | 24 | 1 | 16 | 8 |