Inhibitor discordance and concordance between siblings in the study cohort of 78 MIBS families
Inhibitor history in each sibling . | Type of hemophilia A . | . | . | . | ||
|---|---|---|---|---|---|---|
| . | Severe . | Moderate . | Mild . | Total . | ||
| Discordant families, no. | 34 | |||||
| HR/No | 20 | 2 | 1 | 23 | ||
| LR/No | 5 | 2 | 1 | 8 | ||
| HR/No/No | 1 | 0 | 0 | 1 | ||
| HR/LR/No | 1 | 0 | 0 | 1 | ||
| HR/No/No/No | 0 | 0 | 1 | 1 | ||
| Concordant families, no. | 44 | |||||
| HR/HR | 11 | 0 | 0 | 11 | ||
| LR/LR | 0 | 0 | 1 | 1 | ||
| HR/LR | 5 | 0 | 1 | 6 | ||
| No/No | 15 | 6 | 1 | 22 | ||
| HR/HR/HR | 1 | 0 | 0 | 1 | ||
| LR/LR/LR | 0 | 1 | 0 | 1 | ||
| No/No/No | 1 | 1 | 0 | 2 | ||
| Total. no. (%) | 60 (76.9) | 12 (15.4) | 6 (7.7) | 78 (100) | ||
Inhibitor history in each sibling . | Type of hemophilia A . | . | . | . | ||
|---|---|---|---|---|---|---|
| . | Severe . | Moderate . | Mild . | Total . | ||
| Discordant families, no. | 34 | |||||
| HR/No | 20 | 2 | 1 | 23 | ||
| LR/No | 5 | 2 | 1 | 8 | ||
| HR/No/No | 1 | 0 | 0 | 1 | ||
| HR/LR/No | 1 | 0 | 0 | 1 | ||
| HR/No/No/No | 0 | 0 | 1 | 1 | ||
| Concordant families, no. | 44 | |||||
| HR/HR | 11 | 0 | 0 | 11 | ||
| LR/LR | 0 | 0 | 1 | 1 | ||
| HR/LR | 5 | 0 | 1 | 6 | ||
| No/No | 15 | 6 | 1 | 22 | ||
| HR/HR/HR | 1 | 0 | 0 | 1 | ||
| LR/LR/LR | 0 | 1 | 0 | 1 | ||
| No/No/No | 1 | 1 | 0 | 2 | ||
| Total. no. (%) | 60 (76.9) | 12 (15.4) | 6 (7.7) | 78 (100) | ||
HR, high-responding inhibitor; LR, low-responding inhibitor; No, no inhibitor history.