Diseases associated with T-LGL leukemia
| Associated diseases . | Frequency, % . |
|---|---|
| Autoimmune diseases | 15-40 |
| RA | 11-36 |
| Sjogren syndrome | CR |
| Polymyositis | CR |
| PMR | CR |
| Multineuritis | CR |
| Vasculitis | CR |
| Endocrinopathy | CR |
| Celiac disease | CR |
| CIBD | CR |
| APECED | CR |
| Autoimmune cytopenia* | 5-10 |
| PRCA | 5 |
| AIHA | < 2 |
| ITP | Rare |
| Cyclic neutropenia | Rare |
| Pulmonary hypertension | Rare |
| Neoplasia | < 10 |
| Solid tumors | < 4 |
| Myelodysplasia | < 4 |
| B-cell malignancies | 5-7 |
| CML treated with dasatinib | Recently described |
| Viral infection (HIV, CMV, HCV, EBV) | Rare |
| Posttransplantation | |
| Solid and hematopoietic stem cell transplantation | Rare |
| Associated diseases . | Frequency, % . |
|---|---|
| Autoimmune diseases | 15-40 |
| RA | 11-36 |
| Sjogren syndrome | CR |
| Polymyositis | CR |
| PMR | CR |
| Multineuritis | CR |
| Vasculitis | CR |
| Endocrinopathy | CR |
| Celiac disease | CR |
| CIBD | CR |
| APECED | CR |
| Autoimmune cytopenia* | 5-10 |
| PRCA | 5 |
| AIHA | < 2 |
| ITP | Rare |
| Cyclic neutropenia | Rare |
| Pulmonary hypertension | Rare |
| Neoplasia | < 10 |
| Solid tumors | < 4 |
| Myelodysplasia | < 4 |
| B-cell malignancies | 5-7 |
| CML treated with dasatinib | Recently described |
| Viral infection (HIV, CMV, HCV, EBV) | Rare |
| Posttransplantation | |
| Solid and hematopoietic stem cell transplantation | Rare |
PMR indicates polymyalgia rheumatica; CIBD, chronic inflammatory bowel disease; APECED, autoimmune polyendocrinopathy-candidosis-ectodermal dystrophy; PRCA, pure red cell aplasia; AIHA, autoimmune hemolytic anemia; ITP, idiopathic thrombocytopenic purpura; CML, chronic myeloid leukemia; CMV, cytomegalovirus; HCV, hepatitis C virus; EBV, Epstein-Barr virus; and CR, case report.
Excluding chronic neutropenia.