Presenting symptoms and features of XLP1 patients with associated mortality
| . | Incidence . | Mortality . |
|---|---|---|
| Presenting symptom | ||
| HLH | 31.9% | 65.5% |
| FIM | 7.7% | 14.3% |
| Lymphoma | 14.3% | 7.7% |
| Dysgammaglobulinemia | 22% | 5% |
| Family history of XLP1 alone | 16.5% | 20% |
| Other | 7.7% | 14.3% |
| Features occurring at any time | ||
| HLH | 35.2% | 65.6% |
| FIM | 9.9% | 22.2% |
| Lymphoma | 24.2% | 9% |
| Dysgammaglobulinemia | 50.5% | 13% |
| Other | 15.4% | 28.6% |
| . | Incidence . | Mortality . |
|---|---|---|
| Presenting symptom | ||
| HLH | 31.9% | 65.5% |
| FIM | 7.7% | 14.3% |
| Lymphoma | 14.3% | 7.7% |
| Dysgammaglobulinemia | 22% | 5% |
| Family history of XLP1 alone | 16.5% | 20% |
| Other | 7.7% | 14.3% |
| Features occurring at any time | ||
| HLH | 35.2% | 65.6% |
| FIM | 9.9% | 22.2% |
| Lymphoma | 24.2% | 9% |
| Dysgammaglobulinemia | 50.5% | 13% |
| Other | 15.4% | 28.6% |