Symptoms of chronic active EBV
| Patient . | Fever . | Lymphadenopathy . | Splenomegaly . | Hepatomegaly . | CNS disease . | Peripheral neuropathy . | Interstitial pneumonitis . | Pancytopenia . | Hepatitis . | Hemophagocytosis . | Hypogammaglobulinemia . | Other . |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| Unknown whether B-, T-, or NK-cell disease | ||||||||||||
| 1 | + | + | + | + | + | + | + | |||||
| 2 | + | + | + | + | + | |||||||
| 4 | + | + | ||||||||||
| 5 | + | + | + | + | Autoimmune hemolytic anemia, sinusitis | |||||||
| B-cell disease | ||||||||||||
| 3 | + | + | + | + | Autoimmune hemolytic anemia, neutropenia, skin disease, vasculitis, sinusitis, thrombocytopenia | |||||||
| 6 | + | + | + | + | + | + | + | + | Uveitis | |||
| 7 | + | + | + | Sinusitis, vasculitis | ||||||||
| 8 | + | + | + | |||||||||
| 9 | + | + | + | + | + | + | + | + | + | |||
| 11 | + | + | + | + | + | + | Autoimmune hemolytic anemia | |||||
| 12 | + | + | + | + | + | + | Eye disease, skin disease | |||||
| 13 | + | + | + | + | + | Skin disease | ||||||
| 14 | + | + | + | |||||||||
| 16 | + | + | + | |||||||||
| 17 | + | + | + | + | Sinusitis | |||||||
| T-cell disease | ||||||||||||
| 10 | + | + | + | + | + | + | + | Sinusitis, thrombocytopenia | ||||
| 15 | + | + | + | Hydroa vacciniforme | ||||||||
| 18 | + | + | + | + | + | Conjunctivitis | ||||||
| NK-cell disease | ||||||||||||
| 19 | Skin disease, mosquito bite hypersensitivity |
| Patient . | Fever . | Lymphadenopathy . | Splenomegaly . | Hepatomegaly . | CNS disease . | Peripheral neuropathy . | Interstitial pneumonitis . | Pancytopenia . | Hepatitis . | Hemophagocytosis . | Hypogammaglobulinemia . | Other . |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| Unknown whether B-, T-, or NK-cell disease | ||||||||||||
| 1 | + | + | + | + | + | + | + | |||||
| 2 | + | + | + | + | + | |||||||
| 4 | + | + | ||||||||||
| 5 | + | + | + | + | Autoimmune hemolytic anemia, sinusitis | |||||||
| B-cell disease | ||||||||||||
| 3 | + | + | + | + | Autoimmune hemolytic anemia, neutropenia, skin disease, vasculitis, sinusitis, thrombocytopenia | |||||||
| 6 | + | + | + | + | + | + | + | + | Uveitis | |||
| 7 | + | + | + | Sinusitis, vasculitis | ||||||||
| 8 | + | + | + | |||||||||
| 9 | + | + | + | + | + | + | + | + | + | |||
| 11 | + | + | + | + | + | + | Autoimmune hemolytic anemia | |||||
| 12 | + | + | + | + | + | + | Eye disease, skin disease | |||||
| 13 | + | + | + | + | + | Skin disease | ||||||
| 14 | + | + | + | |||||||||
| 16 | + | + | + | |||||||||
| 17 | + | + | + | + | Sinusitis | |||||||
| T-cell disease | ||||||||||||
| 10 | + | + | + | + | + | + | + | Sinusitis, thrombocytopenia | ||||
| 15 | + | + | + | Hydroa vacciniforme | ||||||||
| 18 | + | + | + | + | + | Conjunctivitis | ||||||
| NK-cell disease | ||||||||||||
| 19 | Skin disease, mosquito bite hypersensitivity |