BLyS receptor expression in WM patients
Patient . | Age, y . | Sex . | Lym . | Spl . | BAFF-R . | BCMA . | TACI . |
|---|---|---|---|---|---|---|---|
| WM1 | 77 | M | No | No | +++ | + | ++ |
| WM2 | 50 | M | No | No | +++ | — | + |
| WM3 | 78 | M | Yes | No | +++ | ++ | ++ |
| WM4 | 83 | M | Yes | No | + | — | + |
| WM5 | 62 | M | No | No | ++ | + | + |
| WM16 | 67 | M | Yes | Yes | + | ++ | — |
| WM17 | 88 | F | No | Yes | + | + | + |
| WM18 | 81 | M | Yes | No | ++ | + | + |
| WM19 | 75 | M | No | No | ++ | + | + |
| WM20 | 88 | F | No | No | ++ | — | — |
| WM21 | 67 | F | No | No | ++ | + | ++ |
| WM22 | 77 | F | No | No | + | — | — |
Patient . | Age, y . | Sex . | Lym . | Spl . | BAFF-R . | BCMA . | TACI . |
|---|---|---|---|---|---|---|---|
| WM1 | 77 | M | No | No | +++ | + | ++ |
| WM2 | 50 | M | No | No | +++ | — | + |
| WM3 | 78 | M | Yes | No | +++ | ++ | ++ |
| WM4 | 83 | M | Yes | No | + | — | + |
| WM5 | 62 | M | No | No | ++ | + | + |
| WM16 | 67 | M | Yes | Yes | + | ++ | — |
| WM17 | 88 | F | No | Yes | + | + | + |
| WM18 | 81 | M | Yes | No | ++ | + | + |
| WM19 | 75 | M | No | No | ++ | + | + |
| WM20 | 88 | F | No | No | ++ | — | — |
| WM21 | 67 | F | No | No | ++ | + | ++ |
| WM22 | 77 | F | No | No | + | — | — |
In all patients, the BLyS receptor bound BLyS.
Lym indicates lymphadenopathy; Spl, splenomegaly; +++, high expression (MFI > 21); +, low expression (MFI, 2-6); ++, intermediate expression (MFI, 7-20); no expression (MFI < 2).
None of the patients used in these studies had any ongoing inflammatory infections that would increase BLyS levels.