Outcome of patients who did not undergo transplantation
| Kindred . | Patient . | Sex . | Age at last follow-up, y . | Status . | Cause of death . | Complications . |
|---|---|---|---|---|---|---|
| 1 | P1 | F | 10 | Dead | Liver failure | ENT infections, pneumonia, bacterial sepsis severe viral infection, chronic diarrhea, liver disease, AIHA |
| 3 | P4 | M | 1 | Dead | Encephalomyelitis | ENT infections, severe viral infection |
| 5 | P6 | M | 32 | Alive | ENT infections, pneumonia, severe viral infection, bacterial meningitis liver disease, AIHA | |
| 6 | P7 | F | 5 | Dead | Severe pneumonia | ENT infections, pneumonia, chronic diarrhea |
| 7 | P8 | M | 17 | Dead | Liver failure | ENT infections, pneumonia, bacterial sepsis, chronic diarrhea, chronic intestinal cryptosporidiosis, liver disease, AIHA |
| 10 | P12 | F | 2 | Dead | Meningoencephalitis | ENT infections, bacterial sepsis, severe viral infection |
| 12 | P14 | M | 23 | Alive | ENT infections, pneumonia, recurrent gastrointestinal infections, liver disease | |
| 31 | P26 | M | 6 | Alive | ENT infections, severe viral infection | |
| 34 | P29 | M | 9 | Alive | ENT infections, pneumonia, chronic diarrhea | |
| 37 | P32 | F | 12 | Alive | Pneumonia, chronic diarrhea, liver disease | |
| 39 | P34 | F | 7 | Alive | Pneumonia, bronchiectasis, chronic intestinal cryptosporidiosis, liver disease | |
| 40 | P35 | M | 16 | Alive | Pneumonia, bronchiectasis |
| Kindred . | Patient . | Sex . | Age at last follow-up, y . | Status . | Cause of death . | Complications . |
|---|---|---|---|---|---|---|
| 1 | P1 | F | 10 | Dead | Liver failure | ENT infections, pneumonia, bacterial sepsis severe viral infection, chronic diarrhea, liver disease, AIHA |
| 3 | P4 | M | 1 | Dead | Encephalomyelitis | ENT infections, severe viral infection |
| 5 | P6 | M | 32 | Alive | ENT infections, pneumonia, severe viral infection, bacterial meningitis liver disease, AIHA | |
| 6 | P7 | F | 5 | Dead | Severe pneumonia | ENT infections, pneumonia, chronic diarrhea |
| 7 | P8 | M | 17 | Dead | Liver failure | ENT infections, pneumonia, bacterial sepsis, chronic diarrhea, chronic intestinal cryptosporidiosis, liver disease, AIHA |
| 10 | P12 | F | 2 | Dead | Meningoencephalitis | ENT infections, bacterial sepsis, severe viral infection |
| 12 | P14 | M | 23 | Alive | ENT infections, pneumonia, recurrent gastrointestinal infections, liver disease | |
| 31 | P26 | M | 6 | Alive | ENT infections, severe viral infection | |
| 34 | P29 | M | 9 | Alive | ENT infections, pneumonia, chronic diarrhea | |
| 37 | P32 | F | 12 | Alive | Pneumonia, chronic diarrhea, liver disease | |
| 39 | P34 | F | 7 | Alive | Pneumonia, bronchiectasis, chronic intestinal cryptosporidiosis, liver disease | |
| 40 | P35 | M | 16 | Alive | Pneumonia, bronchiectasis |