Patient response to administration of DDAVP
Patient no. . | Amino acid . | DDAVP . | VWF:Ag, IU/dL . | VWF:RCo, IU/dL . | VWF:RCo/VWF:Ag . | FVIII:C, IU/dL . |
---|---|---|---|---|---|---|
2 | M740I*/C1190S/I1380V | Pre | 184 | 34 | 0.2 | 146 |
Post (1 h) | 258 | 128 | 0.5 | 300 | ||
Post (4 h) | 248 | 100 | 0.4 | 238 | ||
10 | I1568N | Pre | 34 | 7 | 0.2 | 37 |
Post (1 h) | 276 | 164 | 0.6 | 235 | ||
Post (4 h) | 176 | 76 | 0.4 | N/A | ||
11 | G1579R | Pre | 52 | 4 | 0.1 | 46 |
Post (1 h) | 232 | 54 | 0.2 | 200 | ||
Post (4 h) | 178 | 30 | 0.2 | 114 |
Patient no. . | Amino acid . | DDAVP . | VWF:Ag, IU/dL . | VWF:RCo, IU/dL . | VWF:RCo/VWF:Ag . | FVIII:C, IU/dL . |
---|---|---|---|---|---|---|
2 | M740I*/C1190S/I1380V | Pre | 184 | 34 | 0.2 | 146 |
Post (1 h) | 258 | 128 | 0.5 | 300 | ||
Post (4 h) | 248 | 100 | 0.4 | 238 | ||
10 | I1568N | Pre | 34 | 7 | 0.2 | 37 |
Post (1 h) | 276 | 164 | 0.6 | 235 | ||
Post (4 h) | 176 | 76 | 0.4 | N/A | ||
11 | G1579R | Pre | 52 | 4 | 0.1 | 46 |
Post (1 h) | 232 | 54 | 0.2 | 200 | ||
Post (4 h) | 178 | 30 | 0.2 | 114 |
N/A indicates not applicable.