Clinical characteristics of study patients
| Pt. no. . | Age at diagnosis, y* . | Sex . | Ethnicity . | SCLS subtype . | Possible associations . | Attack frequency per year . | Treatment regimen . | Severe attacks . |
|---|---|---|---|---|---|---|---|---|
| 1 | 45 | M | W | Classic acute | None | > 2 times | IVIG since 2/10 | Y |
| 2 | 49 | F | W | Classic acute | None | Frequent | Theophylline + terbutaline | Y |
| 3 | 45 | M | W | Classic acute | None | Frequent | Theophylline + terbutaline | Y |
| 4 | 55 | M | W | Classic acute | None | > 2 times | IVIG since 11/09 | Y |
| 5 | 46 | F | W | Classic acute | None | Frequent | Multiple (deceased) | Y |
| 6 | 42 | M | W | Classic acute | None | < 1 time | Theophylline | Y |
| 7 | 32 | M | W | Classic acute | URI | < 2 times | Theophylline + terbutaline | Y |
| 8 | 59 | M | W | Classic acute | None | < 2 times | Theophylline + terbutaline | Y |
| 9 | 65 | M | W | Classic acute | None | > 2 times | Theophylline + terbutaline | Y |
| 10 | 39 | F | W | Chronic and acute | None | Chronic | Theophylline + terbutaline | Y |
| 11 | 53 | F | W | Classic acute | URI | < 1 time | Theophylline + terbutaline | Y |
| 12 | 48 | M | W | Classic acute | URI, eating tenderized meat | Frequent | IVIG since 5/10 | Y |
| 13 | 50 | F | W | Classic acute | None | > 2 times | Theophylline + terbutaline | Y |
| 14 | 53 | M | W | Classic acute | None | > 2 times | IVIG × 6 y | Y |
| 15 | 53 | M | W | Classic acute | None | Frequent | IVIG since 9/09 | Y |
| 16 | 39 | F | W | Chronic | None | Chronic | Theophylline + terbutaline | N |
| 17 | 43 | F | W | Classic acute | Influenza (seropositive) | < 2 times | None | Y |
| 18 | 60 | F | W | Chronic | Chronic | Theophylline + terbutaline | N | |
| 19 | 48 | M | AA | Classic acute | None | > 2 times | Theophylline + terbutaline | Y |
| 20 | 43 | M | W | Classic acute | None | Frequent | Theophylline + terbutaline | Y |
| 21 | 65 | M | W | Classic acute | WNV (seropositive) | < 2 times | Theophylline | Y |
| 22 | 43 | M | W | Classic acute | None | < 2 times | Theophylline | Y |
| 23 | 47 | F | W | Classic acute | None | < 2 times | Theophylline | Y |
| Pt. no. . | Age at diagnosis, y* . | Sex . | Ethnicity . | SCLS subtype . | Possible associations . | Attack frequency per year . | Treatment regimen . | Severe attacks . |
|---|---|---|---|---|---|---|---|---|
| 1 | 45 | M | W | Classic acute | None | > 2 times | IVIG since 2/10 | Y |
| 2 | 49 | F | W | Classic acute | None | Frequent | Theophylline + terbutaline | Y |
| 3 | 45 | M | W | Classic acute | None | Frequent | Theophylline + terbutaline | Y |
| 4 | 55 | M | W | Classic acute | None | > 2 times | IVIG since 11/09 | Y |
| 5 | 46 | F | W | Classic acute | None | Frequent | Multiple (deceased) | Y |
| 6 | 42 | M | W | Classic acute | None | < 1 time | Theophylline | Y |
| 7 | 32 | M | W | Classic acute | URI | < 2 times | Theophylline + terbutaline | Y |
| 8 | 59 | M | W | Classic acute | None | < 2 times | Theophylline + terbutaline | Y |
| 9 | 65 | M | W | Classic acute | None | > 2 times | Theophylline + terbutaline | Y |
| 10 | 39 | F | W | Chronic and acute | None | Chronic | Theophylline + terbutaline | Y |
| 11 | 53 | F | W | Classic acute | URI | < 1 time | Theophylline + terbutaline | Y |
| 12 | 48 | M | W | Classic acute | URI, eating tenderized meat | Frequent | IVIG since 5/10 | Y |
| 13 | 50 | F | W | Classic acute | None | > 2 times | Theophylline + terbutaline | Y |
| 14 | 53 | M | W | Classic acute | None | > 2 times | IVIG × 6 y | Y |
| 15 | 53 | M | W | Classic acute | None | Frequent | IVIG since 9/09 | Y |
| 16 | 39 | F | W | Chronic | None | Chronic | Theophylline + terbutaline | N |
| 17 | 43 | F | W | Classic acute | Influenza (seropositive) | < 2 times | None | Y |
| 18 | 60 | F | W | Chronic | Chronic | Theophylline + terbutaline | N | |
| 19 | 48 | M | AA | Classic acute | None | > 2 times | Theophylline + terbutaline | Y |
| 20 | 43 | M | W | Classic acute | None | Frequent | Theophylline + terbutaline | Y |
| 21 | 65 | M | W | Classic acute | WNV (seropositive) | < 2 times | Theophylline | Y |
| 22 | 43 | M | W | Classic acute | None | < 2 times | Theophylline | Y |
| 23 | 47 | F | W | Classic acute | None | < 2 times | Theophylline | Y |
Pt indicates patient; W, white; IVIG, intravenous immunoglobulin; Y, yes; URI, upper respiratory infection; N, no; AA, African American; and WNV, West Nile virus.
Several patients experienced episodes consistent with SCLS before formal diagnosis.