Table 2

Response of patients with hematological AD to first-line treatment

Steroids onlyRTXCSARTX + CSAIVIgOthers
ITP NR (n = 1) CR (n = 2) NR (n = 1) CR (n = 2)  NR (n = 1) NR (n = 1) PR (n = 3)  
AIHA NR (n = 1) PR (n = 2) CR (n = 1) NR (n = 1) PR (n = 1) PR (n = 2)* CR (n = 5) CR (n = 2) PR (n = 1) NR (n = 1)* PR (n = 1) PR (n = 1) CSA + tacrolimus CR (n = 1) 
Evans  NR (n = 1) CR (n = 1) NR (n = 2) PR (n = 1) CR (n = 1)  PR (n = 1) CR (n = 1) Tacrolimus PR (n = 1) 
Steroids onlyRTXCSARTX + CSAIVIgOthers
ITP NR (n = 1) CR (n = 2) NR (n = 1) CR (n = 2)  NR (n = 1) NR (n = 1) PR (n = 3)  
AIHA NR (n = 1) PR (n = 2) CR (n = 1) NR (n = 1) PR (n = 1) PR (n = 2)* CR (n = 5) CR (n = 2) PR (n = 1) NR (n = 1)* PR (n = 1) PR (n = 1) CSA + tacrolimus CR (n = 1) 
Evans  NR (n = 1) CR (n = 1) NR (n = 2) PR (n = 1) CR (n = 1)  PR (n = 1) CR (n = 1) Tacrolimus PR (n = 1) 

ITP indicates immune thrombocytopenia; AIHA, autoimmune hemolytic anemia; RTX, rituximab; CSA, cyclosporine A; NR, no response; PR, partial response; and CR, complete response.

*

Received additional plasmapheresis.

Received additional CSA.

Received additional cyclophosphamide.

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