Table 3

Response of patients with hematological AD to second-line therapy

Steroids onlyRTXOther
ITP CR (n = 1) PR (n = 1)
NN (n = 1)
NN (n = 1) + azathioprine
CR (n = 1) 
PR (n = 1) plasma exchange 
AIHA NR (n = 1)
PR (n = 2)
CR (n = 2) 
Azathioprine (n = 1) NN
CSA (n = 1) CR 
Evans NR (n = 1) + cyclophosphamide
PR (n = 1) + CSA + tacrolimus
CR (n = 1) + CSA + MMF
PR (n = 1)
CR (n = 2) + tacrolimus 
 
Steroids onlyRTXOther
ITP CR (n = 1) PR (n = 1)
NN (n = 1)
NN (n = 1) + azathioprine
CR (n = 1) 
PR (n = 1) plasma exchange 
AIHA NR (n = 1)
PR (n = 2)
CR (n = 2) 
Azathioprine (n = 1) NN
CSA (n = 1) CR 
Evans NR (n = 1) + cyclophosphamide
PR (n = 1) + CSA + tacrolimus
CR (n = 1) + CSA + MMF
PR (n = 1)
CR (n = 2) + tacrolimus 
 

MMF indicates mycophenolate mofetil; and NN, response not known.

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