The first clinical manifestations leading to an assignment of a score of 5 in the first 2 years of life (N = 26)
| Manifestation at onset of a score of 5 . | n . | % . |
|---|---|---|
| SRT only | 12 | 46 |
| AIHA only | 3 | 12 |
| AIHA + profound thrombocytopenia* | 3 | 12 |
| Autoimmune pancytopenia | 3 | 12 |
| Vasculitis only | 4 | 15 |
| Vasculitis + SRT | 1 | 4 |
| Tumor only | 0 | 0 |
| Manifestation at onset of a score of 5 . | n . | % . |
|---|---|---|
| SRT only | 12 | 46 |
| AIHA only | 3 | 12 |
| AIHA + profound thrombocytopenia* | 3 | 12 |
| Autoimmune pancytopenia | 3 | 12 |
| Vasculitis only | 4 | 15 |
| Vasculitis + SRT | 1 | 4 |
| Tumor only | 0 | 0 |
SRT indicates severe refractory thrombocytopenia (platelet count < 10 G/L); profound thrombocytopenia, a platelet count of between 10 and 20 G/L; and AIHA, autoimmune hemolytic anemia.