Vasculitis in patients with severe WAS in the first 2 years of life
| Patient . | Manifestation(s) . | Age, mo . | Therapy . |
|---|---|---|---|
| P5 | Joints, skin, gut | 22 | IV CS → CR → relapse → CR → HSCT |
| P7 | Brain | 11 | IV CS → PR → CS + Cy → CR → HSCT |
| P9 | Joints, skin | 14 | IV CS → CR → AIHA → HSCT |
| P15 | Lungs, skin | 2 | IV CS → CR → HSCT |
| P17 | Joints, skin, high fever | 17 | IV CS → CR → AIHA → HSCT |
| P18 | Joints, skin, high fever | 9 | IV CS → PR → CS + IVIgs → CR → HSCT |
| Patient . | Manifestation(s) . | Age, mo . | Therapy . |
|---|---|---|---|
| P5 | Joints, skin, gut | 22 | IV CS → CR → relapse → CR → HSCT |
| P7 | Brain | 11 | IV CS → PR → CS + Cy → CR → HSCT |
| P9 | Joints, skin | 14 | IV CS → CR → AIHA → HSCT |
| P15 | Lungs, skin | 2 | IV CS → CR → HSCT |
| P17 | Joints, skin, high fever | 17 | IV CS → CR → AIHA → HSCT |
| P18 | Joints, skin, high fever | 9 | IV CS → PR → CS + IVIgs → CR → HSCT |
Cy indicates cyclophosphamide.