Clinical characteristics (N = 134)
| Parameter . | Value . |
|---|---|
| Mean age at diagnosis (y) | 62 (range 17-85) |
| Gender | 76 M:58 F |
| LGL count (103/μL) | 2324 ± 2932 |
| Splenomegaly | 29% (39/134) |
| TCR rearrangement by PCR | 97% (123/126) |
| STAT3 mutation | 18% (19/105) |
| Hematologic manifestation | 87% (116/134) |
| Anemia | 67% (90/134) |
| Neutropenia | 49% (65/134) |
| Thromobocytopenia | 31% (42/134) |
| Multilineage cytopenia | 27% (36/134) |
| Pancytopenia | 18% (24/134) |
| Lymphocytosis | 30% (40/134) |
| Lymphopenia | 16% (22/134) |
| B-cell or antibody disorder | 49% (65/134) |
| Monoclonal gammopathy of unknown significance/multiple myeloma | 16% (22/134) |
| Hypergammaglobunemia | 16% (22/134) |
| Hypogammaglobunemia | 8% (11/134) |
| Chronic lymphocytic leukemia | 10% (13/134) |
| Hairy cell leukemia | <1% (1/134) |
| Non-Hodgkin lymphoma | 1% (2/134) |
| B-cell lymphoma/lymphoproliferative disorder | 1% (2/134) |
| Autoimmune disease | 18% (24/134) |
| Rheumatoid arthritis | 14% (19/134) |
| Myasthenia gravis, Guillain-Barre | 1% (2/134) |
| Pernicious anemia, autoimmune hemolytic anemia | 1% (2/134) |
| Sjögren, Crohn, Felty | 2% (3/134) |
| Parameter . | Value . |
|---|---|
| Mean age at diagnosis (y) | 62 (range 17-85) |
| Gender | 76 M:58 F |
| LGL count (103/μL) | 2324 ± 2932 |
| Splenomegaly | 29% (39/134) |
| TCR rearrangement by PCR | 97% (123/126) |
| STAT3 mutation | 18% (19/105) |
| Hematologic manifestation | 87% (116/134) |
| Anemia | 67% (90/134) |
| Neutropenia | 49% (65/134) |
| Thromobocytopenia | 31% (42/134) |
| Multilineage cytopenia | 27% (36/134) |
| Pancytopenia | 18% (24/134) |
| Lymphocytosis | 30% (40/134) |
| Lymphopenia | 16% (22/134) |
| B-cell or antibody disorder | 49% (65/134) |
| Monoclonal gammopathy of unknown significance/multiple myeloma | 16% (22/134) |
| Hypergammaglobunemia | 16% (22/134) |
| Hypogammaglobunemia | 8% (11/134) |
| Chronic lymphocytic leukemia | 10% (13/134) |
| Hairy cell leukemia | <1% (1/134) |
| Non-Hodgkin lymphoma | 1% (2/134) |
| B-cell lymphoma/lymphoproliferative disorder | 1% (2/134) |
| Autoimmune disease | 18% (24/134) |
| Rheumatoid arthritis | 14% (19/134) |
| Myasthenia gravis, Guillain-Barre | 1% (2/134) |
| Pernicious anemia, autoimmune hemolytic anemia | 1% (2/134) |
| Sjögren, Crohn, Felty | 2% (3/134) |