Contingency table representing outcome of DS patients by NCI risk group and PdL risk group criteria
| Classical NCI criteria . | PdL risk criteria . | . | |
|---|---|---|---|
| Standard risk . | High risk . | ||
| Low risk | n = 187 EFS 78% ± 3% OS 87% ± 3% TRM 3% ± 1% CIR 17% ± 3% | n = 246 EFS 63% ± 4% OS 73% ± 3% TRM 7% ± 2% CIR 30% ± 4% | NCI SR n = 433 |
| High risk | n = 0 | n = 218 EFS 57% ± 4% OS 62% ± 4% TRM 12% ± 2% CIR 29% ± 3% | NCI HR n = 218 |
| PdL SR model n = 187 | PdL HR model n = 464 | Total n = 651 | |
| Classical NCI criteria . | PdL risk criteria . | . | |
|---|---|---|---|
| Standard risk . | High risk . | ||
| Low risk | n = 187 EFS 78% ± 3% OS 87% ± 3% TRM 3% ± 1% CIR 17% ± 3% | n = 246 EFS 63% ± 4% OS 73% ± 3% TRM 7% ± 2% CIR 30% ± 4% | NCI SR n = 433 |
| High risk | n = 0 | n = 218 EFS 57% ± 4% OS 62% ± 4% TRM 12% ± 2% CIR 29% ± 3% | NCI HR n = 218 |
| PdL SR model n = 187 | PdL HR model n = 464 | Total n = 651 | |
Classical NCI risk criteria: age 1-9 or ≥ 10 y at diagnosis and WBC < or ≥50 × 109/L; PdL low-risk criteria: age <6 y and WBC <10 × 109/L; PdL high-risk criteria: all other patients.
HR, high risk; SR, standard risk.