Table 3

Summary of peripheral blood counts and immunophenotyping of GATA2 and AA patients

FeaturesGATA2AAP
Hemoglobin (median, g/L; normal range 137-175 g/L) 105.00 94.00 .03 
Platelets (median, x 109/L; normal range 161-347 109/L) 115.00 23.00 <.0001 
WBC (median, 109/L; normal range 4.23-9.07 109/L) 2.57 2.25 .7054 
Neutrophils (median, 109/L; normal range 1.56-6.13 109/L) 1.55 0.62 <.001 
Monocytes (median, 109/L; normal range 0.30-0.82 109/L) 0.01 0.10 <.001 
Lymphocytes (median, 109/L; normal range 1.18-3.74 109/L) 0.67 1.45 <.0001 
B cells (median, % lymphs; normal range 6-19%) (median, 109/L; normal range 0.07- 0.71 109/L) 0.50 9.40 <.0001 
0.003 0.13 <.0001 
T cells (median, % lymphs; normal range 57-79%) (median, 109/L; normal range 0.67- 2.95 109/L) 98.10 82.60 <.0001 
0.59 1.17 <.0001 
NK cells (median, % lymphs; normal range 7-31%) (median, 109/L; normal range 0.08- 1.15 109/L) 0.50 5.60 <.0001 
0.003165 0.09122 <.0001 
FeaturesGATA2AAP
Hemoglobin (median, g/L; normal range 137-175 g/L) 105.00 94.00 .03 
Platelets (median, x 109/L; normal range 161-347 109/L) 115.00 23.00 <.0001 
WBC (median, 109/L; normal range 4.23-9.07 109/L) 2.57 2.25 .7054 
Neutrophils (median, 109/L; normal range 1.56-6.13 109/L) 1.55 0.62 <.001 
Monocytes (median, 109/L; normal range 0.30-0.82 109/L) 0.01 0.10 <.001 
Lymphocytes (median, 109/L; normal range 1.18-3.74 109/L) 0.67 1.45 <.0001 
B cells (median, % lymphs; normal range 6-19%) (median, 109/L; normal range 0.07- 0.71 109/L) 0.50 9.40 <.0001 
0.003 0.13 <.0001 
T cells (median, % lymphs; normal range 57-79%) (median, 109/L; normal range 0.67- 2.95 109/L) 98.10 82.60 <.0001 
0.59 1.17 <.0001 
NK cells (median, % lymphs; normal range 7-31%) (median, 109/L; normal range 0.08- 1.15 109/L) 0.50 5.60 <.0001 
0.003165 0.09122 <.0001 
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