Table 1

Risk of death in LPL/WM patients in relation to family history of LPs

No. of patientsHR*95% CI
Family history of    
 Any LP 93 1.34 1.03-1.75 
  Per increasing number of relatives  1.22 0.99-1.50 
 Multiple myeloma 13 1.47 0.76-2.85 
 Non-Hodgkin lymphoma 44 1.43 1.00-2.06 
 Hodgkin lymphoma 0.51 0.13-2.03 
 Chronic lymphocytic leukemia 17 1.43 0.71-2.88 
 LPL/WM 16 1.28 0.69-2.39 
 Monoclonal gammopathy of undetermined significance 11 1.12 0.53-2.37 
 Any LP (age scale)  1.32 1.02-172 
 Any LP (year-of-diagnosis scale)  1.31 1.01-1.71 
Age at diagnosis (per 1-year increase)  1.06 1.05-1.07 
Female gender  0.72 0.65-0.79 
Year of diagnosis (per 1-year increase)  0.99 0.98-1.00 
No. of patientsHR*95% CI
Family history of    
 Any LP 93 1.34 1.03-1.75 
  Per increasing number of relatives  1.22 0.99-1.50 
 Multiple myeloma 13 1.47 0.76-2.85 
 Non-Hodgkin lymphoma 44 1.43 1.00-2.06 
 Hodgkin lymphoma 0.51 0.13-2.03 
 Chronic lymphocytic leukemia 17 1.43 0.71-2.88 
 LPL/WM 16 1.28 0.69-2.39 
 Monoclonal gammopathy of undetermined significance 11 1.12 0.53-2.37 
 Any LP (age scale)  1.32 1.02-172 
 Any LP (year-of-diagnosis scale)  1.31 1.01-1.71 
Age at diagnosis (per 1-year increase)  1.06 1.05-1.07 
Female gender  0.72 0.65-0.79 
Year of diagnosis (per 1-year increase)  0.99 0.98-1.00 
*

Cox model adjusted for age at diagnosis, gender, and year of diagnosis.

The additive risk of each first-degree family member diagnosed with an LP.

Family members with non-Hodgkin lymphoma, excluding those with LPL/WM.

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