Main characteristics of patients from group A and B
. | All patients . | Group A . | Group B . | P . |
---|---|---|---|---|
No. | 79 | 39 | 40 | |
Sex ratio, M/F | 1.51 | 1.44 | 1.67 | NS |
Mean age at diagnosis, mo | 19 ± 4.9 | 8.5 ± 3.7 | 30 ± 8.8 | * |
Protein | Ankyrin = 18 | Ankyrin = 11 | Ankyrin = 7 | NS |
Band 3 = 1 | Band 3 = 0 | Band 3 = 1 | ||
Protein 4.2 = 1 | Protein 4.2 = 0 | Protein 4.2 = 1 | ||
α-Spectrin = 2 | α-Spectrin = 2 | α-Spectrin = 0 | ||
β-Spectrin = 12 | β-Spectrin = 7 | β-Spectrin = 5 | ||
Mean hemoglobin, g/L | 97 ± 2.2 | 83 ± 1.9 | 110 ± 2.6 | **** |
Mean reticulocytes, G/L | 392 ± 18 | 391 ± 26 | 393 ± 24 | NS |
Mean total bilirubin, µmol/L | 59 ± 6 | 47 ± 6.9 | 68 ± 9 | NS |
Mean no. of transfusion per year | 1.6 ± 0.4 | 3.1 ± 0.7 | 0.13 ± 0.02 | **** |
Lithiasis, % | 32.1 | 20.0 | 47.5 | ** |
Mean age at surgery, y | 7.4 ± 0.6 | 4.3 ± 0.6 | 11 ± 0.7 | **** |
Mean time of follow-up, y | 11 ± 0.7 | 12 ± 0.9 | 9.3 ± 1.0 | NS |
. | All patients . | Group A . | Group B . | P . |
---|---|---|---|---|
No. | 79 | 39 | 40 | |
Sex ratio, M/F | 1.51 | 1.44 | 1.67 | NS |
Mean age at diagnosis, mo | 19 ± 4.9 | 8.5 ± 3.7 | 30 ± 8.8 | * |
Protein | Ankyrin = 18 | Ankyrin = 11 | Ankyrin = 7 | NS |
Band 3 = 1 | Band 3 = 0 | Band 3 = 1 | ||
Protein 4.2 = 1 | Protein 4.2 = 0 | Protein 4.2 = 1 | ||
α-Spectrin = 2 | α-Spectrin = 2 | α-Spectrin = 0 | ||
β-Spectrin = 12 | β-Spectrin = 7 | β-Spectrin = 5 | ||
Mean hemoglobin, g/L | 97 ± 2.2 | 83 ± 1.9 | 110 ± 2.6 | **** |
Mean reticulocytes, G/L | 392 ± 18 | 391 ± 26 | 393 ± 24 | NS |
Mean total bilirubin, µmol/L | 59 ± 6 | 47 ± 6.9 | 68 ± 9 | NS |
Mean no. of transfusion per year | 1.6 ± 0.4 | 3.1 ± 0.7 | 0.13 ± 0.02 | **** |
Lithiasis, % | 32.1 | 20.0 | 47.5 | ** |
Mean age at surgery, y | 7.4 ± 0.6 | 4.3 ± 0.6 | 11 ± 0.7 | **** |
Mean time of follow-up, y | 11 ± 0.7 | 12 ± 0.9 | 9.3 ± 1.0 | NS |
F, female; g/L, grams per liter; G/L, giga per liter; M, male; NS, not significant.
*P < .05; **P < .01; ****P < .0001.