Clinical Features in LDGL Patients With a Low Number of GL (<2,000/μL) as Compared With Findings Detected in Cases With Typical Disorder
| Variable . | Patients With Low GL Count . | Typical LDGL Patients . | ||
|---|---|---|---|---|
| . | (<2,000/μL) . | (>2,000/μL) . | ||
| . | Observed . | % . | Observed . | % . |
| Sex (female/male) | 6/5 | 65/86 | ||
| Associated diseases | 8/11 | 72.7 | 82/151 | 45.6 |
| Systemic B symptoms | 1/11 | 9.0 | 41/151 | 27.1 |
| Recurrent infections | 6/11 | 54.5 | 93/151 | 61.5 |
| Oral ulcers | 1/11 | 9.0 | 7/151 | 4.6 |
| Splenomegaly | 5/11 | 45.4 | 66/132 | 50.0 |
| Hepatomegaly | 1/11 | 9.0 | 51/151 | 33.7 |
| Lymphadenopathy | 0/11 | 0 | 19/132 | 14.3 |
| Skin involvement | 0/11 | 0 | 5/146 | 3.4 |
| Therapy required | 9/11 | 81.8 | 45/151 | 29.8 |
| Response to therapy | ||||
| Complete | 0/9 | 0 | 1/45 | 2.2 |
| Partial | 5/9 | 55.5 | 18/45 | 40.0 |
| Variable . | Patients With Low GL Count . | Typical LDGL Patients . | ||
|---|---|---|---|---|
| . | (<2,000/μL) . | (>2,000/μL) . | ||
| . | Observed . | % . | Observed . | % . |
| Sex (female/male) | 6/5 | 65/86 | ||
| Associated diseases | 8/11 | 72.7 | 82/151 | 45.6 |
| Systemic B symptoms | 1/11 | 9.0 | 41/151 | 27.1 |
| Recurrent infections | 6/11 | 54.5 | 93/151 | 61.5 |
| Oral ulcers | 1/11 | 9.0 | 7/151 | 4.6 |
| Splenomegaly | 5/11 | 45.4 | 66/132 | 50.0 |
| Hepatomegaly | 1/11 | 9.0 | 51/151 | 33.7 |
| Lymphadenopathy | 0/11 | 0 | 19/132 | 14.3 |
| Skin involvement | 0/11 | 0 | 5/146 | 3.4 |
| Therapy required | 9/11 | 81.8 | 45/151 | 29.8 |
| Response to therapy | ||||
| Complete | 0/9 | 0 | 1/45 | 2.2 |
| Partial | 5/9 | 55.5 | 18/45 | 40.0 |