Clinical Features and Laboratory Data at Accelerated Phase in Patients With HLH
| Case . | 1 . | 2 . | 3 . | 4 . | 5 . | 6 . | 7 . | 8 . | 9 . | 10 . | 11 . |
|---|---|---|---|---|---|---|---|---|---|---|---|
| Sex | M | M | M | M | M | F | F | M | M | M | M |
| Age | 1 yr | 4 yr | 8 mo | 10 yr | 5 yr | 8 mo | 10 yr | 2 yr | 7 yr | 2 yr | 2 yr |
| Clinical features | |||||||||||
| Fever | + | + | + | + | + | + | + | + | + | + | + |
| Hepatomegaly | + | + | + | + | + | + | + | + | + | + | + |
| Splenomegaly | + | + | + | + | + | + | + | + | + | + | + |
| DIC | + | + | + | + | + | + | + | + | − | − | − |
| Outcome | Dead | Dead | Dead | Dead | Alive | Alive | Alive | Alive | Alive | Alive | Alive |
| Laboratory data | |||||||||||
| Pancytopenia | + | + | + | + | + | + | + | + | + | + | + |
| Liver dysfunction | + | + | + | + | + | + | + | + | + | + | + |
| Hyperferritinemia | + | + | + | + | + | + | + | + | + | + | + |
| Hypertriglyceridemia | + | + | + | + | + | + | + | + | + | − | − |
| Case . | 1 . | 2 . | 3 . | 4 . | 5 . | 6 . | 7 . | 8 . | 9 . | 10 . | 11 . |
|---|---|---|---|---|---|---|---|---|---|---|---|
| Sex | M | M | M | M | M | F | F | M | M | M | M |
| Age | 1 yr | 4 yr | 8 mo | 10 yr | 5 yr | 8 mo | 10 yr | 2 yr | 7 yr | 2 yr | 2 yr |
| Clinical features | |||||||||||
| Fever | + | + | + | + | + | + | + | + | + | + | + |
| Hepatomegaly | + | + | + | + | + | + | + | + | + | + | + |
| Splenomegaly | + | + | + | + | + | + | + | + | + | + | + |
| DIC | + | + | + | + | + | + | + | + | − | − | − |
| Outcome | Dead | Dead | Dead | Dead | Alive | Alive | Alive | Alive | Alive | Alive | Alive |
| Laboratory data | |||||||||||
| Pancytopenia | + | + | + | + | + | + | + | + | + | + | + |
| Liver dysfunction | + | + | + | + | + | + | + | + | + | + | + |
| Hyperferritinemia | + | + | + | + | + | + | + | + | + | + | + |
| Hypertriglyceridemia | + | + | + | + | + | + | + | + | + | − | − |