Results of platelet function tests in pedigree
Family member . | Serotonin (μmol/1011platelets) . | ADP . | ATP . | Bleeding time (min/150 × 109 platelets) . | Platelet aggregation . |
---|---|---|---|---|---|
(μmol/1011 platelets) . | |||||
II:1 | 439 | 3.1 | 5.2 | 5 | Good |
II:3 | 366 | 2.5 | 5.0 | 5 | Good |
II:4 | |||||
Before SCT | 197 | 0.5 | 3.8 | > 30 | Very poor |
After SCT | 189 | 1.0 | 5.2 | na | Very poor |
II:7 | 440 | 1.4 | 5.2 | > 30 | Very poor |
II:8 | 305 | 0.9 | 4.4 | > 30 | Very poor |
Normal range | 200-600 | 1.7-3.0 | 3.1-7.0 | 7 |
Family member . | Serotonin (μmol/1011platelets) . | ADP . | ATP . | Bleeding time (min/150 × 109 platelets) . | Platelet aggregation . |
---|---|---|---|---|---|
(μmol/1011 platelets) . | |||||
II:1 | 439 | 3.1 | 5.2 | 5 | Good |
II:3 | 366 | 2.5 | 5.0 | 5 | Good |
II:4 | |||||
Before SCT | 197 | 0.5 | 3.8 | > 30 | Very poor |
After SCT | 189 | 1.0 | 5.2 | na | Very poor |
II:7 | 440 | 1.4 | 5.2 | > 30 | Very poor |
II:8 | 305 | 0.9 | 4.4 | > 30 | Very poor |
Normal range | 200-600 | 1.7-3.0 | 3.1-7.0 | 7 |
SCT indicates stem cell transplantation; na, not analyzed.