Table 3.

Engraftment status

Primary diseaseAll diseases, n (%)
HLH, n (%)Other PID, n (%)
Total (n) 34 12 46 
Sustained engraftment    
 Sustained donor chimerism >5%, alive at 1 y, no intervention 14 (41) 4 (33) 18 (39) 
Received DLI and/or second HCT    
 Donor chimerism >5% after intervention 9 (26) 1 (8) 10 (22) 
 Donor chimerism ≤5% after intervention 3 (9) 2 (17) 5 (11) 
Primary graft failure    
 Donor chimerism remained ≤5% after initial HCT 1 (3) 1 (8) 2 (4) 
Secondary graft failure    
 Donor chimerism ≤5% without intervention 1 (3) 1 (8) 2 (4) 
Not evaluable for sustained engraftment    
 Donor chimerism 53% at day 28, died before day 42 1 (3) 0 (0) 1 (2) 
 Sustained donor chimerism >5%, dead before 1 y 5 (15) 3 (25) 8 (17) 
Primary diseaseAll diseases, n (%)
HLH, n (%)Other PID, n (%)
Total (n) 34 12 46 
Sustained engraftment    
 Sustained donor chimerism >5%, alive at 1 y, no intervention 14 (41) 4 (33) 18 (39) 
Received DLI and/or second HCT    
 Donor chimerism >5% after intervention 9 (26) 1 (8) 10 (22) 
 Donor chimerism ≤5% after intervention 3 (9) 2 (17) 5 (11) 
Primary graft failure    
 Donor chimerism remained ≤5% after initial HCT 1 (3) 1 (8) 2 (4) 
Secondary graft failure    
 Donor chimerism ≤5% without intervention 1 (3) 1 (8) 2 (4) 
Not evaluable for sustained engraftment    
 Donor chimerism 53% at day 28, died before day 42 1 (3) 0 (0) 1 (2) 
 Sustained donor chimerism >5%, dead before 1 y 5 (15) 3 (25) 8 (17) 

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