Clinical characteristics of the patients
. | Patient 1 . | Patient 2 . | Patient 3 . |
---|---|---|---|
Age, y | |||
At the onset of symptoms | 33 | 28 | 37 |
At the time of LT | 36 | 39 | 42 |
Sex | Female | Female | Female |
Smoking status (pack-years) | Former smoker (1) | Nonsmoker | Former smoker (8) |
Environment or occupational exposure | Not found | Not found | Not found |
Adenopathies | (−) | (−) | (−) |
Splenomegaly | (−) | (−) | (−) |
Hepatomegaly | (−) | (−) | (−) |
Viral status, serology | |||
HCV infection | (−) | (−) | (−) |
HIV infection | (−) | (−) | (−) |
Monoclonal IG before LT* | |||
Serum | Free κ light chain | (−) | (−) |
Urine | (−) | ND | ND |
Serum IgG, IgA, IgM levels | Normal | Normal | Normal |
Bone marrow plasmocytes, % | < 5 | < 5 | < 5 |
Renal function (serum creatinine level, μmol/L) | Normal (50) | Normal (55) | Normal (100) |
Proteinuria, mg/d | 70 | 60 | 200 |
Liver function tests | Normal | Normal | Normal |
Heart function† | Normal | Normal | Normal |
Extrapulmonary deposits | |||
Bone marrow | (−) | (−) | (−) |
Salivary glands | + | (−) | + |
Skin | ¤ | (−) | ¤ |
Duodenum | ¤ | (−) | ¤ |
Rectum | ¤ | (−) | ¤ |
Kidney | ¤ | ¤ | (−) |
Autologous blood stem cell transplantation before LT | No | Yes‡ | No |
Follow up, mo | 39 | 69 | 33 |
Monoclonal IG after LT* | |||
Serum | (−) | (−) | (−) |
Urine | (−) | (−) | (−) |
Recurrence of the disease | No | No | No |
. | Patient 1 . | Patient 2 . | Patient 3 . |
---|---|---|---|
Age, y | |||
At the onset of symptoms | 33 | 28 | 37 |
At the time of LT | 36 | 39 | 42 |
Sex | Female | Female | Female |
Smoking status (pack-years) | Former smoker (1) | Nonsmoker | Former smoker (8) |
Environment or occupational exposure | Not found | Not found | Not found |
Adenopathies | (−) | (−) | (−) |
Splenomegaly | (−) | (−) | (−) |
Hepatomegaly | (−) | (−) | (−) |
Viral status, serology | |||
HCV infection | (−) | (−) | (−) |
HIV infection | (−) | (−) | (−) |
Monoclonal IG before LT* | |||
Serum | Free κ light chain | (−) | (−) |
Urine | (−) | ND | ND |
Serum IgG, IgA, IgM levels | Normal | Normal | Normal |
Bone marrow plasmocytes, % | < 5 | < 5 | < 5 |
Renal function (serum creatinine level, μmol/L) | Normal (50) | Normal (55) | Normal (100) |
Proteinuria, mg/d | 70 | 60 | 200 |
Liver function tests | Normal | Normal | Normal |
Heart function† | Normal | Normal | Normal |
Extrapulmonary deposits | |||
Bone marrow | (−) | (−) | (−) |
Salivary glands | + | (−) | + |
Skin | ¤ | (−) | ¤ |
Duodenum | ¤ | (−) | ¤ |
Rectum | ¤ | (−) | ¤ |
Kidney | ¤ | ¤ | (−) |
Autologous blood stem cell transplantation before LT | No | Yes‡ | No |
Follow up, mo | 39 | 69 | 33 |
Monoclonal IG after LT* | |||
Serum | (−) | (−) | (−) |
Urine | (−) | (−) | (−) |
Recurrence of the disease | No | No | No |
LT indicates lung transplantation; HCV, hepatitis C virus; HIV, human immunodeficiency virus; (−), absent; ND; not done; +, present; and ¤, no biopsy performed.
Protein electrophoresis and immunofixation.
Evaluated by echocardiography and right cardiac catheterization.
Without improvement or stabilization.