Table 3

Clinical characteristics of CTEPH patients with fibrinogen variants

Patient IDFibrinogen variantAge, y/sexHistory*SeverityDuration of symptomsPVR, dyn•s/cm5
Plasma fibrinogen, mg/dL
PreopPostopClaussAntigen
San Diego I 23/M No Severe 7 y 311 157 94 96 
San Diego II 45/F No Moderate 9 mo 1175 378 319 317 
San Diego III 54/F Yes Mild 18 mo 1570 172 260 244 
San Diego IV 49/M Yes Mild 20 mo 679 166 NA NA 
San Diego V 33/F No Moderate 8 mo 772 242 367 451 
Patient IDFibrinogen variantAge, y/sexHistory*SeverityDuration of symptomsPVR, dyn•s/cm5
Plasma fibrinogen, mg/dL
PreopPostopClaussAntigen
San Diego I 23/M No Severe 7 y 311 157 94 96 
San Diego II 45/F No Moderate 9 mo 1175 378 319 317 
San Diego III 54/F Yes Mild 18 mo 1570 172 260 244 
San Diego IV 49/M Yes Mild 20 mo 679 166 NA NA 
San Diego V 33/F No Moderate 8 mo 772 242 367 451 

PVR indicates pulmonary vascular resistance; and NA, not available.

*

Family history of acute thrombosis.

Severity of initial acute PE: severe indicates unstable in ICU; moderate, hospitalized; and mild, outpatient.

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