Sensitivity and specificity of immunohistochemistry
| . | Clinical diagnosis . | Typical symptoms of AL . | Monoclonal gammopathy . | Positive genotyping . | Positive family history . | Sensitivity . | Specificity . |
|---|---|---|---|---|---|---|---|
| AL amyloidosis | 39 | 39 | 39 | 0 | 0 | 39/39 | 39/39 |
| ATTR amyloidosis | 5 | 0 | 0 | 5 | 2 | 4/5 | 4/4 |
| AApoA1 amyloidosis | 2 | 0 | 0 | 2 | 1 | 2/2 | 2/2 |
| AFib amyloidosis | 4 | 0 | 0 | 4 | 1 | 3/4 | 3/3 |
| AA amyloidosis | 1 | 0 | 0 | 0 | 0 | 1/1 | 1/1 |
| . | Clinical diagnosis . | Typical symptoms of AL . | Monoclonal gammopathy . | Positive genotyping . | Positive family history . | Sensitivity . | Specificity . |
|---|---|---|---|---|---|---|---|
| AL amyloidosis | 39 | 39 | 39 | 0 | 0 | 39/39 | 39/39 |
| ATTR amyloidosis | 5 | 0 | 0 | 5 | 2 | 4/5 | 4/4 |
| AApoA1 amyloidosis | 2 | 0 | 0 | 2 | 1 | 2/2 | 2/2 |
| AFib amyloidosis | 4 | 0 | 0 | 4 | 1 | 3/4 | 3/3 |
| AA amyloidosis | 1 | 0 | 0 | 0 | 0 | 1/1 | 1/1 |
Data are anamnestic, clinical, and laboratory results of the first group of 51 patients with a known amyloid subentity as well as immunohistochemical results.