Table 2.

vWF Properties

SubjectAg (%)RiCof*(%)MultimersBlood Type
Father 195 167 Normal pattern 
Mother 84 54 Absence of HMWM 
Patient 86 50 Absence of HMWM 
Younger sister 37 17 Absence of HMWM 
SubjectAg (%)RiCof*(%)MultimersBlood Type
Father 195 167 Normal pattern 
Mother 84 54 Absence of HMWM 
Patient 86 50 Absence of HMWM 
Younger sister 37 17 Absence of HMWM 
*

Ristocetin cofactor activity.

High-molecular-weight multimers.

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