Relative Frequency and 5-Year Survival of the Main Groups of Primary Cutaneous Lymphoma Included in the EORTC Classification
| Classification . | No. . | Frequency (%) . | 5-Year Survival3-150 (%) . |
|---|---|---|---|
| MF | 278 | 44 | 87 |
| Specific variants of MF | |||
| MF + mucinosis follicularis | 30 | 4 | 70 |
| Pagetoid reticulosis | 5 | <1 | 100 |
| Granulomatous slack skin | 2 | <1 | — |
| CTCL, large cell (CD30+) | 57 | 9 | 90 |
| Lymphomatoid papulosis | 70 | 11 | 100 |
| CTCL, large cell (CD30−) | 36 | 5 | 15 |
| SS | 12 | 2 | 11 |
| CTCL, pleomorphic small/med | 18 | 3 | 62 |
| CBCL, PCFCCL3-151 | 84 | 13 | 97 |
| Immunocytoma (MZBCL) | 12 | 2 | 100 |
| LBCL of the legs | 18 | 3 | 58 |
| Intravascular B-cell lymphoma | 4 | <1 | 50 |
| Classification . | No. . | Frequency (%) . | 5-Year Survival3-150 (%) . |
|---|---|---|---|
| MF | 278 | 44 | 87 |
| Specific variants of MF | |||
| MF + mucinosis follicularis | 30 | 4 | 70 |
| Pagetoid reticulosis | 5 | <1 | 100 |
| Granulomatous slack skin | 2 | <1 | — |
| CTCL, large cell (CD30+) | 57 | 9 | 90 |
| Lymphomatoid papulosis | 70 | 11 | 100 |
| CTCL, large cell (CD30−) | 36 | 5 | 15 |
| SS | 12 | 2 | 11 |
| CTCL, pleomorphic small/med | 18 | 3 | 62 |
| CBCL, PCFCCL3-151 | 84 | 13 | 97 |
| Immunocytoma (MZBCL) | 12 | 2 | 100 |
| LBCL of the legs | 18 | 3 | 58 |
| Intravascular B-cell lymphoma | 4 | <1 | 50 |
Data are based on 626 patients with a primary cutaneous lymphoma registered at the Dutch Cutaneous Lymphoma Working Group between 1986 and 1994.
Abbreviations: CTCL, cutaneous T-cell lymphoma; CBCL, cutaneous B-cell lymphoma; PCFCCL, primary cutaneous follicle center cell lymphoma; LBCL, large B-cell lymphoma; MZBCL, marginal zone B-cell lymphoma; MF, mycosis fungoides; SS, Sezary syndrome.
The figures presented represent the disease-related 5-year survival.
Excluding follicle center cell lymphomas on the legs.