Table 1.

Clinical Findings and Laboratory Values of the 14 Patients With AL Amyloidosis Studied

Patients Age (yr) Main Organ Involved-150Monoclonal Component BMPC % BMPC k/λ Ratio-151BMPC LI%
QUA  59  Heart  BJκ  7  49.0 0.2  
TAU  49  Kidney, liver  BJκ  10  5.41 ND  
IAC  55  Liver  BJκ  4  61.5  0.2 
ORR  65  Heart  BJκ  10  7.3  0.0  
DIB 70  Kidney  BJλ  7  0.28  0.1  
PAP  53 GI  BJλ  10  0.2  ND  
SEM  46  Muscle, GI BJλ  5  0.02  0.2  
FER  51  Muscle, GI BJλ  3  0.11  0.0  
GHE  78  Heart  BJλ 10  0.02  0.1  
FIL  57  Heart  BJλ  0.07  0.0  
CAR  62  Skin, nerves  IgGκ + BJκ 10  40.67  0.0  
SET  56  Lung  IgGλ  0.67  0.4  
MAR  73  Heart  IgAλ  7  0.13 ND  
DEP  48  Skin, heart  IgAλ + BJλ  10 0.23  0.2 
Patients Age (yr) Main Organ Involved-150Monoclonal Component BMPC % BMPC k/λ Ratio-151BMPC LI%
QUA  59  Heart  BJκ  7  49.0 0.2  
TAU  49  Kidney, liver  BJκ  10  5.41 ND  
IAC  55  Liver  BJκ  4  61.5  0.2 
ORR  65  Heart  BJκ  10  7.3  0.0  
DIB 70  Kidney  BJλ  7  0.28  0.1  
PAP  53 GI  BJλ  10  0.2  ND  
SEM  46  Muscle, GI BJλ  5  0.02  0.2  
FER  51  Muscle, GI BJλ  3  0.11  0.0  
GHE  78  Heart  BJλ 10  0.02  0.1  
FIL  57  Heart  BJλ  0.07  0.0  
CAR  62  Skin, nerves  IgGκ + BJκ 10  40.67  0.0  
SET  56  Lung  IgGλ  0.67  0.4  
MAR  73  Heart  IgAλ  7  0.13 ND  
DEP  48  Skin, heart  IgAλ + BJλ  10 0.23  0.2 

Abbreviations: GI, gastrointestinal tract; BMPC, bone marrow PC; LI%, labeling index; ND, not determined.

F0-150

Main organ involved at diagnosis.

F0-151

Normal values are ≥1.1, ≤2.6.7 

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