vWF Abnormal Fragments Found in Samples From Patients With Familial HUS/TTP With an MoAb (RG5) Recognizing the C Terminus of vWF Subunit
Patient . | Disease Phase . | Abnormal Fragments . |
---|---|---|
F34#1 | Remission | No |
F45#2 | Remission | Yes (150 kD4-150) |
F39#3 | Acute | No |
Remission | No | |
F40#3 | Remission | No |
F30#4 | Remission | Yes (150 kD4-150) |
F33#4 | Remission | No |
F64#5 | Remission | No |
F1#6 | Remission | No |
F101#19 | Acute | No |
F102#19 | Remission | Yes (150 kD4-150) |
F106#24 | Remission | Yes (150 kD4-150) |
F108#24 | Remission | No |
F29#29a | Remission | Yes (140 kD4-150) |
F85#29b | Remission | No |
Patient . | Disease Phase . | Abnormal Fragments . |
---|---|---|
F34#1 | Remission | No |
F45#2 | Remission | Yes (150 kD4-150) |
F39#3 | Acute | No |
Remission | No | |
F40#3 | Remission | No |
F30#4 | Remission | Yes (150 kD4-150) |
F33#4 | Remission | No |
F64#5 | Remission | No |
F1#6 | Remission | No |
F101#19 | Acute | No |
F102#19 | Remission | Yes (150 kD4-150) |
F106#24 | Remission | Yes (150 kD4-150) |
F108#24 | Remission | No |
F29#29a | Remission | Yes (140 kD4-150) |
F85#29b | Remission | No |
Presumed molecular weight extrapolated from the position of the band on gel.