Table 1.

Summary of methionine hemoglobin (MetHb) level, b5R activity, and relative b5R content of the family

SubjectII.3II.4 II.6 II.7 III.1 III.2III.3 III.4 III.5 III.9 III.10 Control
MetHb/total Hb (%)  20.9  19.0  3.75  15.2  3.30 1.43  2.94  3.30  2.94  1.78  2.06  < 2 
b5R activity (IU/g Hb)* 0.84  0.9  2.5  2.8  6.5 8.9  8.5  10.1  7.4  10.5  12.1 12.5-22.2  
Relative b5R content 0  NS  0  NS  NS  NS NS  0.53  0.56  0.36  1.0 
SubjectII.3II.4 II.6 II.7 III.1 III.2III.3 III.4 III.5 III.9 III.10 Control
MetHb/total Hb (%)  20.9  19.0  3.75  15.2  3.30 1.43  2.94  3.30  2.94  1.78  2.06  < 2 
b5R activity (IU/g Hb)* 0.84  0.9  2.5  2.8  6.5 8.9  8.5  10.1  7.4  10.5  12.1 12.5-22.2  
Relative b5R content 0  NS  0  NS  NS  NS NS  0.53  0.56  0.36  1.0 

NS indicates not studied.

*

b5R activity was measured as NADH-ferricyanide activity.

b5R protein amount is expressed as relative to that of the normal control.

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