Summary of methionine hemoglobin (MetHb) level, b5R activity, and relative b5R content of the family
Subject . | II.3 . | II.4 . | II.6 . | II.7 . | III.1 . | III.2 . | III.3 . | III.4 . | III.5 . | III.9 . | III.10 . | Control . |
---|---|---|---|---|---|---|---|---|---|---|---|---|
MetHb/total Hb (%) | 20.9 | 19.0 | 3.75 | 15.2 | 3.30 | 1.43 | 2.94 | 3.30 | 2.94 | 1.78 | 2.06 | < 2 |
b5R activity (IU/g Hb)* | 0.84 | 0.9 | 2.5 | 2.8 | 6.5 | 8.9 | 8.5 | 10.1 | 7.4 | 10.5 | 12.1 | 12.5-22.2 |
Relative b5R content† | 0 | 0 | NS | 0 | NS | NS | NS | NS | 0.53 | 0.56 | 0.36 | 1.0 |
Subject . | II.3 . | II.4 . | II.6 . | II.7 . | III.1 . | III.2 . | III.3 . | III.4 . | III.5 . | III.9 . | III.10 . | Control . |
---|---|---|---|---|---|---|---|---|---|---|---|---|
MetHb/total Hb (%) | 20.9 | 19.0 | 3.75 | 15.2 | 3.30 | 1.43 | 2.94 | 3.30 | 2.94 | 1.78 | 2.06 | < 2 |
b5R activity (IU/g Hb)* | 0.84 | 0.9 | 2.5 | 2.8 | 6.5 | 8.9 | 8.5 | 10.1 | 7.4 | 10.5 | 12.1 | 12.5-22.2 |
Relative b5R content† | 0 | 0 | NS | 0 | NS | NS | NS | NS | 0.53 | 0.56 | 0.36 | 1.0 |