Associated lymphomas in patients with lymphomatoid papulosis
Patient . | Sex/age (y) . | Associated lymphoma . | Time interval3-150 (y) . | Localization . | Therapy . | Current status (follow-up in mo) . | ||
---|---|---|---|---|---|---|---|---|
Skin . | ec . | Lymphoma . | LyP . | |||||
1 | F/48 | CD30+ LTCL | B (5) | − | + | RT | A0 (120) | A+ (57) |
2 | M/46 | CD30+ LTCL | A (1) | + | − | RT | A0 (81) | A+ (94) |
3 | M/28 | CD30+ LTCL | A (25, 27) | + | − | RT/None3-151 | A0 (50, 20) | A+ (350) |
4 | F/24 | CD30+ LTCL | A (2, 3) | + | − | None3-151 | A0 (57, 43) | A+ (77) |
5 | M/12 | CD30+ LTCL | A (1) | + | − | None3-151 | A0 (4) | A+ (21) |
6 | M/23 | CD30+ LTCL | A (1) | + | +3-152 | CHOP | A0 (144) | A+ (156) |
7 | M/31 | CD30+ LTCL | A (5) | + | + | CHOP | A0 (39) | A+ (99) |
8 | F/53 | CD30+ LTCL | A (1) | + | +3-152 | None3-151 | A0 (105) | A+ (115) |
9 | M/43 | CD30+ LTCL | A (1) | + | +3-152 | None3-151 | A0 (14) | A+ (27) |
10 | M/52 | CD30+ LTCL | A (18) | + | + | CHOP | D+ (12) | D+ (228) |
11 | F/64 | Hodgkin disease | A (6) | − | + | MOPP | D0 (77) | D0 (142) |
12 | M/33 | Hodgkin disease | A (13) | − | + | MOPP | D+ (6) | D+ (168) |
13 | M/38 | Mycosis fungoides (Ib) | A (4) | + | − | PUVA | A+ (98) | A+ (142) |
14 | F/72 | Mycosis fungoides (Ib) | B (4) | + | − | RT | A+ (143) | A0 (97) |
15 | F/56 | Mycosis fungoides (Ib) | A (10) | + | − | HN2 | A0 (244) | A+ (118) |
16 | M/45 | Mycosis fungoides (Ia) | A (4) | + | − | HN2 | A+ (131) | A+ (177) |
17 | F/88 | Mycosis fungoides (Ib) | C | + | − | Retinoids + PUVA | D0 (23) | D0 (23) |
18 | M/73 | Mycosis Fungoides (Ib) | A (8) | + | − | UVB | A0 (102) | A0 (199) |
19 | F/24 | Mycosis Fungoides (Ib) | C | + | − | PUVA | A+ (94) | A+ (94) |
20 | M/59 | Mycosis Fungoides (Ib) | A (12) | + | − | TSEB | A0 (218) | A+ (77) |
21 | M/64 | Mycosis Fungoides (Ia) | A (2) | + | − | UVB | A+ (34) | A+ (55) |
22 | M/51 | Mycosis Fungoides (Ib) | C | + | − | PUVA | A+ (20) | A+ (20) |
23 | M/73 | Mycosis Fungoides (Ib) | B (8) | + | − | PUVA | D0 (160) | D0 (78) |
Patient . | Sex/age (y) . | Associated lymphoma . | Time interval3-150 (y) . | Localization . | Therapy . | Current status (follow-up in mo) . | ||
---|---|---|---|---|---|---|---|---|
Skin . | ec . | Lymphoma . | LyP . | |||||
1 | F/48 | CD30+ LTCL | B (5) | − | + | RT | A0 (120) | A+ (57) |
2 | M/46 | CD30+ LTCL | A (1) | + | − | RT | A0 (81) | A+ (94) |
3 | M/28 | CD30+ LTCL | A (25, 27) | + | − | RT/None3-151 | A0 (50, 20) | A+ (350) |
4 | F/24 | CD30+ LTCL | A (2, 3) | + | − | None3-151 | A0 (57, 43) | A+ (77) |
5 | M/12 | CD30+ LTCL | A (1) | + | − | None3-151 | A0 (4) | A+ (21) |
6 | M/23 | CD30+ LTCL | A (1) | + | +3-152 | CHOP | A0 (144) | A+ (156) |
7 | M/31 | CD30+ LTCL | A (5) | + | + | CHOP | A0 (39) | A+ (99) |
8 | F/53 | CD30+ LTCL | A (1) | + | +3-152 | None3-151 | A0 (105) | A+ (115) |
9 | M/43 | CD30+ LTCL | A (1) | + | +3-152 | None3-151 | A0 (14) | A+ (27) |
10 | M/52 | CD30+ LTCL | A (18) | + | + | CHOP | D+ (12) | D+ (228) |
11 | F/64 | Hodgkin disease | A (6) | − | + | MOPP | D0 (77) | D0 (142) |
12 | M/33 | Hodgkin disease | A (13) | − | + | MOPP | D+ (6) | D+ (168) |
13 | M/38 | Mycosis fungoides (Ib) | A (4) | + | − | PUVA | A+ (98) | A+ (142) |
14 | F/72 | Mycosis fungoides (Ib) | B (4) | + | − | RT | A+ (143) | A0 (97) |
15 | F/56 | Mycosis fungoides (Ib) | A (10) | + | − | HN2 | A0 (244) | A+ (118) |
16 | M/45 | Mycosis fungoides (Ia) | A (4) | + | − | HN2 | A+ (131) | A+ (177) |
17 | F/88 | Mycosis fungoides (Ib) | C | + | − | Retinoids + PUVA | D0 (23) | D0 (23) |
18 | M/73 | Mycosis Fungoides (Ib) | A (8) | + | − | UVB | A0 (102) | A0 (199) |
19 | F/24 | Mycosis Fungoides (Ib) | C | + | − | PUVA | A+ (94) | A+ (94) |
20 | M/59 | Mycosis Fungoides (Ib) | A (12) | + | − | TSEB | A0 (218) | A+ (77) |
21 | M/64 | Mycosis Fungoides (Ia) | A (2) | + | − | UVB | A+ (34) | A+ (55) |
22 | M/51 | Mycosis Fungoides (Ib) | C | + | − | PUVA | A+ (20) | A+ (20) |
23 | M/73 | Mycosis Fungoides (Ib) | B (8) | + | − | PUVA | D0 (160) | D0 (78) |
Associated lymphoma before (B), after (A), or concurrent (C) with the development of lymphomatoid papulosis.
Complete spontaneous resolution before initiation therapy.
Involved draining lymph node only.
ec, extracutaneous; LyP, lymphomatoid papulosis; CD30+LTCL, CD30+ large T-cell lymphoma; RT, radiotherapy; A0, alive no evidence of disease; A+, alive with disease; D0, died of unrelated disease; D+, died of lymphoma; CHOP, cyclophosphamide, doxorubicin, vincristine, prednisone; MOPP, mechlorethamine, vincristine, procarbazine, prednisone; HN2, topical nitrogen mustard; TSEB, total skin electron beam irradiation; mycosis fungoides, in all patients patch/plaque stage MF affecting <10% (Ia) or >10% (Ib) of the skin surface.